Cogan syndrome (Q96638)

Vasculitis occurring in patients with Cogan's syndrome. Cogan’s syndrome is characterised by ocular inflammatory lesions, including interstitial keratitis, uveitis, and episcleritis, and inner ear disease, including sensorineural hearing loss and vestibular dysfunction. Vasculitic manifestations may include arteritis (affecting small, medium or large arteries), aortitis, aortic aneurysms, and aortic and mitral valvulitis.