Diffuse cutaneous mastocytosis (Q94594)

From determinar.ia.br - Determine suas informações
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously.
Language Label Description Also known as
default for all languages
ID_193128939
    English
    Diffuse cutaneous mastocytosis
    Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously.

      Statements

      CID11:ID_193128939
      0 references
      dki-india-ID_193128939
      0 references
      Concluído
      0 references
      15 August 2026
      0 references