Haemophilia B (Q39577)
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Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor IX deficiency. Depending on the extent of the factor IX deficiency, it can be severe (biological activity of factor IX below 1%), moderately severe (activity of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%).
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 3B11.0 |
||
| English | Haemophilia B |
Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor IX deficiency. Depending on the extent of the factor IX deficiency, it can be severe (biological activity of factor IX below 1%), moderately severe (activity of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%). |
Statements
CID11:3B11.0
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dki-india-3B11.0
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Concluído
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13 August 2026
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