Gerstmann-Straussler-Scheinker syndrome (Q38208)

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A disease caused by inheritance of mutation(s) in normal prion protein genes. This disease is characterised by cerebellar ataxia, decreased coordination, dysmetria, or dysarthria, and is fatal. Confirmation is by pathological examination of the brain and genetic testing.
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8E02.1
    English
    Gerstmann-Straussler-Scheinker syndrome
    A disease caused by inheritance of mutation(s) in normal prion protein genes. This disease is characterised by cerebellar ataxia, decreased coordination, dysmetria, or dysarthria, and is fatal. Confirmation is by pathological examination of the brain and genetic testing.

      Statements

      CID11:8E02.1
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      dki-india-8E02.1
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      Concluído
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      13 August 2026
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