Left heart obstruction at multiple sites (Q105073): Difference between revisions
From determinar.ia.br - Determine suas informações
Created a new Item |
Changed label, description and/or aliases in pt-br, en |
||
| description / pt-br | description / pt-br | ||
Malformação cardiovascular congênita em que mais de uma das seguintes lesões estão presentes no coração normalmente conectado: (1) anel mitral supravalvar ou intravalvar, (2) estenose valvar mitral, (3) estenose subvalvar mitral, incluindo uma deformidade em paraquedas da valva mitral, (4) estenose subaórtica, (5) estenose aórtica valvar, (6) estenose aórtica supravalvar e (7) coarctação aórtica._x000D_ _x000D_ Informações adicionais: A obstrução do coração esquerdo em várias localizações, também conhecida como síndrome de Shone, consiste em hipoplasia multinível ou obstrução das estruturas do coração esquerdo. Essa entidade está baseada no relatório original de Shone (1963) que analisou 8 casos de autópsia e descreveu a tendência de coexistência de múltiplas condições obstrutivas, ou potencialmente obstrutivas. Apenas 2 dos 8 casos exibiram quatro condições, com os outros casos exibindo apenas duas ou três das anomalias. | |||
| description / en | description / en | ||
A congenital cardiovascular malformation in which more than one of the following lesions are present in the normally connected heart: (1) supravalvar or intravalvar mitral ring, (2) mitral valvar stenosis, (3) mitral subvalvar stenosis, including a parachute deformity of the mitral valve, (4) subaortic stenosis, (5) valvar aortic stenosis, (6) supravalvar aortic stenosis and (7) aortic coarctation. Additional information: Left heart obstruction at multiple sites, also known as Shone syndrome, consists of multilevel hypoplasia or obstruction of left heart structures. This entity is based on the original report from Shone (1963) that analysed 8 autopsied cases and described the tendency of multiple obstructive, or potentially obstructive, conditions to coexist. Only 2 of the 8 cases exhibited four conditions, with the other cases exhibiting only two or three of the anomalies. | |||
Revision as of 10:59, 17 August 2026
A congenital cardiovascular malformation in which more than one of the following lesions are present in the normally connected heart: (1) supravalvar or intravalvar mitral ring, (2) mitral valvar stenosis, (3) mitral subvalvar stenosis, including a parachute deformity of the mitral valve, (4) subaortic stenosis, (5) valvar aortic stenosis, (6) supravalvar aortic stenosis and (7) aortic coarctation. Additional information: Left heart obstruction at multiple sites, also known as Shone syndrome, consists of multilevel hypoplasia or obstruction of left heart structures. This entity is based on the original report from Shone (1963) that analysed 8 autopsied cases and described the tendency of multiple obstructive, or potentially obstructive, conditions to coexist. Only 2 of the 8 cases exhibited four conditions, with the other cases exhibiting only two or three of the anomalies.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_295410302 |
||
| English | Left heart obstruction at multiple sites |
A congenital cardiovascular malformation in which more than one of the following lesions are present in the normally connected heart: (1) supravalvar or intravalvar mitral ring, (2) mitral valvar stenosis, (3) mitral subvalvar stenosis, including a parachute deformity of the mitral valve, (4) subaortic stenosis, (5) valvar aortic stenosis, (6) supravalvar aortic stenosis and (7) aortic coarctation. Additional information: Left heart obstruction at multiple sites, also known as Shone syndrome, consists of multilevel hypoplasia or obstruction of left heart structures. This entity is based on the original report from Shone (1963) that analysed 8 autopsied cases and described the tendency of multiple obstructive, or potentially obstructive, conditions to coexist. Only 2 of the 8 cases exhibited four conditions, with the other cases exhibiting only two or three of the anomalies. |
