{"entities":{"Q105073":{"pageid":95471,"ns":120,"title":"Item:Q105073","lastrevid":606582,"modified":"2026-08-17T10:59:26Z","type":"item","id":"Q105073","labels":{"mul":{"language":"mul","value":"ID_295410302"},"pt-br":{"language":"pt-br","value":"Obstru\u00e7\u00e3o card\u00edaca esquerda em v\u00e1rias localiza\u00e7\u00f5es"},"en":{"language":"en","value":"Left heart obstruction at multiple sites"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Malforma\u00e7\u00e3o cardiovascular cong\u00eanita em que mais de uma das seguintes les\u00f5es est\u00e3o presentes no cora\u00e7\u00e3o normalmente conectado: (1) anel mitral supravalvar ou intravalvar, (2) estenose valvar mitral, (3) estenose subvalvar mitral, incluindo uma deformidade em paraquedas da valva mitral, (4) estenose suba\u00f3rtica, (5) estenose a\u00f3rtica valvar, (6) estenose a\u00f3rtica supravalvar e (7) coarcta\u00e7\u00e3o a\u00f3rtica._x000D_ _x000D_ Informa\u00e7\u00f5es adicionais: A obstru\u00e7\u00e3o do cora\u00e7\u00e3o esquerdo em v\u00e1rias localiza\u00e7\u00f5es, tamb\u00e9m conhecida como s\u00edndrome de Shone, consiste em hipoplasia multin\u00edvel ou obstru\u00e7\u00e3o das estruturas do cora\u00e7\u00e3o esquerdo. Essa entidade est\u00e1 baseada no relat\u00f3rio original de Shone (1963) que analisou 8 casos de aut\u00f3psia e descreveu a tend\u00eancia de coexist\u00eancia de m\u00faltiplas condi\u00e7\u00f5es obstrutivas, ou potencialmente obstrutivas. Apenas 2 dos 8 casos exibiram quatro condi\u00e7\u00f5es, com os outros casos exibindo apenas duas ou tr\u00eas das anomalias."},"en":{"language":"en","value":"A congenital cardiovascular malformation in which more than one of the following lesions are present in the normally connected heart: (1) supravalvar or intravalvar mitral ring, (2) mitral valvar stenosis, (3) mitral subvalvar stenosis, including a parachute deformity of the mitral valve, (4) subaortic stenosis, (5) valvar aortic stenosis, (6) supravalvar aortic stenosis and (7) aortic coarctation.  Additional information: Left heart obstruction at multiple sites, also known as Shone syndrome, consists of multilevel hypoplasia or obstruction of left heart structures. This entity is based on the original report from Shone (1963) that analysed 8 autopsied cases and described the tendency of multiple obstructive, or potentially obstructive, conditions to coexist. Only 2 of the 8 cases exhibited four conditions, with the other cases exhibiting only two or three of the anomalies."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"2b1977098b8da07b8bee816825a06d62ebca9756","datavalue":{"value":"https://id.who.int/icd/entity/295410302","type":"string"},"datatype":"url"},"type":"statement","id":"Q105073$5921E1A9-0FE8-4DAC-8A0E-AABD507B19B4","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"bd55b815df7d0ce64a4fc4b760907a82340e2ce3","datavalue":{"value":"CID11:ID_295410302","type":"string"},"datatype":"string"},"type":"statement","id":"Q105073$A29B742D-A870-44EB-8726-95C3D9B098C3","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"623a5b984d836f9db0ca8990a800a220aeb3e9ad","datavalue":{"value":"dki-india-ID_295410302","type":"string"},"datatype":"string"},"type":"statement","id":"Q105073$8A0CEB77-71F0-4D33-A77B-E7C28B7D0784","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q105073$7C946AA0-A5AB-400D-B68E-4FE203B636C6","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q105073$0CD82E70-6E98-4CCB-AAF1-75A9C68B2A8B","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q105073$7398C515-F804-45F6-9243-EF511A9A1C65","rank":"normal"}]},"sitelinks":{}}}}