Dementia due to neurodegeneration with brain iron accumulation (Q99877): Difference between revisions
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Revision as of 16:33, 16 August 2026
Dementia due to abnormal metabolism of iron, particularly affecting the basal ganglia. The main subtypes are Pantothenate Kinase-Associated Neurodegeneration (PKAN) and PLA2G6-Associated Neurodegeneration (PLAN). Onset is typically early in life but can occur in adults. The clinical presentation includes a wide variety of movement disorders.
| Language | Label | Description | Also known as |
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| default for all languages | ID_948552848 |
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| English | Dementia due to neurodegeneration with brain iron accumulation |
Dementia due to abnormal metabolism of iron, particularly affecting the basal ganglia. The main subtypes are Pantothenate Kinase-Associated Neurodegeneration (PKAN) and PLA2G6-Associated Neurodegeneration (PLAN). Onset is typically early in life but can occur in adults. The clinical presentation includes a wide variety of movement disorders. |
