{"entities":{"Q99877":{"pageid":90270,"ns":120,"title":"Item:Q99877","lastrevid":568993,"modified":"2026-08-16T16:33:35Z","type":"item","id":"Q99877","labels":{"mul":{"language":"mul","value":"ID_948552848"},"pt-br":{"language":"pt-br","value":"Dem\u00eancia devida \u00e0 neurodegenera\u00e7\u00e3o com ac\u00famulo cerebral de ferro"},"en":{"language":"en","value":"Dementia due to neurodegeneration with brain iron accumulation"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Dem\u00eancia devida a metabolismo anormal do ferro, afetando particularmente os g\u00e2nglios da base. Os subtipos principais s\u00e3o neurodegenera\u00e7\u00e3o associada a pantontenato quinase (PKAN) e neurodegenera\u00e7\u00e3o associada a PLA2G6 (PLAN). Tipicamente, o in\u00edcio ocorre cedo na vida, mas pode ocorrer em adultos. A apresenta\u00e7\u00e3o cl\u00ednica inclui uma grande variedade de transtornos do movimento."},"en":{"language":"en","value":"Dementia due to abnormal metabolism of iron, particularly affecting the basal ganglia. The main subtypes are Pantothenate Kinase-Associated Neurodegeneration (PKAN) and PLA2G6-Associated Neurodegeneration (PLAN). Onset is typically early in life but can occur in adults. The clinical presentation includes a wide variety of movement disorders."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"5f736c8340edbcf5c93f7b33c47cf4c30065fe69","datavalue":{"value":"https://id.who.int/icd/entity/948552848","type":"string"},"datatype":"url"},"type":"statement","id":"Q99877$FB0E20AE-4AB0-4732-9684-27F1A9B3C0FB","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"7156157a75d5d9cdc2c87d6eb8c5ec47f3ffacc1","datavalue":{"value":"CID11:ID_948552848","type":"string"},"datatype":"string"},"type":"statement","id":"Q99877$07873AFA-69AF-4AFA-8464-AD3FE45C2443","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"df11ef4c93d870ef98b535dd08a50de3f573f95d","datavalue":{"value":"dki-india-ID_948552848","type":"string"},"datatype":"string"},"type":"statement","id":"Q99877$651A541E-CB5C-4320-A234-6C901F353D20","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q99877$0198FACB-6798-43FF-BBEF-7A7C9C8A820F","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q99877$AA9EF241-A0F4-484F-98EC-10A04917393B","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q99877$DA592968-0E20-4ECB-A3B0-CDB80EAA717A","rank":"normal"}]},"sitelinks":{}}}}