Juvenile dermatomyositis with necrotising cutaneous vasculitis (Q92493): Difference between revisions
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Revision as of 07:37, 16 August 2026
Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_504741085 |
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| English | Juvenile dermatomyositis with necrotising cutaneous vasculitis |
Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form. |
