{"entities":{"Q92493":{"pageid":82886,"ns":120,"title":"Item:Q92493","lastrevid":515547,"modified":"2026-08-16T07:37:57Z","type":"item","id":"Q92493","labels":{"mul":{"language":"mul","value":"ID_504741085"},"pt-br":{"language":"pt-br","value":"Dermatomiosite juvenil com vasculite necrosante cut\u00e2nea"},"en":{"language":"en","value":"Juvenile dermatomyositis with necrotising cutaneous vasculitis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Tipo de miopatia inflamat\u00f3ria idiop\u00e1tica caracterizada por erup\u00e7\u00e3o cut\u00e2nea acompanhada de fraqueza muscular, anorexia e fadiga. A forma juvenil apresenta-se de maneira mais insidiosa com fraqueza muscular, particularmente dos flexores do pesco\u00e7o, frequentemente precedida por fadiga e febre baixa. Associado a erup\u00e7\u00e3o heliotr\u00f3pica, eritema periorbit\u00e1rio, p\u00e1pulas de Gottron sobre a face extensora das articula\u00e7\u00f5es metacarpofal\u00e2ngicas e interfal\u00e2ngicas, cotovelos e joelhos e telangectasias periungueais. A forma juvenil est\u00e1 associada a maior envolvimento de vasos sangu\u00edneos e vasculopatia em compara\u00e7\u00e3o com a forma do adulto."},"en":{"language":"en","value":"Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"2c950aa56d904930d908e452362654ddd4038e56","datavalue":{"value":"https://id.who.int/icd/entity/504741085","type":"string"},"datatype":"url"},"type":"statement","id":"Q92493$EEE20EAD-10B6-426E-AD2D-6A6D9513CA84","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"d52de2446e1e30e3021329c895f671711cc5ffb3","datavalue":{"value":"CID11:ID_504741085","type":"string"},"datatype":"string"},"type":"statement","id":"Q92493$E5038DFD-807F-4883-9CC5-23D88E4B3413","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"34c45be2ed34a4d73da0173f2b4d6c604f8028f7","datavalue":{"value":"dki-india-ID_504741085","type":"string"},"datatype":"string"},"type":"statement","id":"Q92493$CA4E78F5-EC0D-41F3-9F6E-F1E4ED14C02B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q92493$21AB5508-878B-42DA-9FBB-7997314A4D31","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q92493$B5154536-1DCD-4052-A42F-7DB83CE86824","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q92493$59EC51C9-CE2F-401A-B864-EB70CBDAE98D","rank":"normal"}]},"sitelinks":{}}}}