Cicatricial pemphigoid, Brunsting-Perry type (Q104444): Difference between revisions
From determinar.ia.br - Determine suas informações
Changed an Item |
Changed an Item |
||
| Property / Knowledge Architect | |||
| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||
Normal rank | |||
Revision as of 10:18, 17 August 2026
A rare scarring immunobullous skin disorder due to autoantibodies to components of the epidermal basement membrane, particularly the anchoring filament component laminin 5 and the hemidesmosome-associated proteins BP180 and BP230. A proportion of patients can be shown to have antibodies to collagen VII and are therefore considered to have a variant of epidermolysis bullosa acquisita (Epidermolysis bullosa acquisita: Brunsting-Perry type).
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1148757980 |
||
| English | Cicatricial pemphigoid, Brunsting-Perry type |
A rare scarring immunobullous skin disorder due to autoantibodies to components of the epidermal basement membrane, particularly the anchoring filament component laminin 5 and the hemidesmosome-associated proteins BP180 and BP230. A proportion of patients can be shown to have antibodies to collagen VII and are therefore considered to have a variant of epidermolysis bullosa acquisita (Epidermolysis bullosa acquisita: Brunsting-Perry type). |
Statements
CID11:ID_1148757980
0 references
dki-india-ID_1148757980
0 references
Concluído
0 references
