{"entities":{"Q104444":{"pageid":94842,"ns":120,"title":"Item:Q104444","lastrevid":602052,"modified":"2026-08-17T10:18:06Z","type":"item","id":"Q104444","labels":{"mul":{"language":"mul","value":"ID_1148757980"},"pt-br":{"language":"pt-br","value":"Penfigoide cicatricial, tipo Brunsting-Perry"},"en":{"language":"en","value":"Cicatricial pemphigoid, Brunsting-Perry type"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Transtorno raro imunobolhoso cicatricial da pele devido a autoanticorpos contra componentes da membrana basal epid\u00e9rmica, particularmente o componente do filamento de ancoragem laminina 5 e as prote\u00ednas associadas ao hemidesmossoma BP180 e BP230. Pode ser demonstrado que uma propor\u00e7\u00e3o de pacientes apresenta anticorpos contra o col\u00e1geno VII e, portanto, considerado que apresentam uma variante da epiderm\u00f3lise bolhosa adquirida (Epiderm\u00f3lise bolhosa adquirida: tipo Brunsting-Perry)."},"en":{"language":"en","value":"A rare scarring immunobullous skin disorder due to autoantibodies to components of the epidermal basement membrane, particularly the anchoring filament component laminin 5 and the hemidesmosome-associated proteins BP180 and BP230. A proportion of patients can be shown to have antibodies to collagen VII and are therefore considered to have a variant of epidermolysis bullosa acquisita (Epidermolysis bullosa acquisita: Brunsting-Perry type)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"1e88ba0208f977142fa554ede1b1758986c88d6f","datavalue":{"value":"https://id.who.int/icd/entity/1148757980","type":"string"},"datatype":"url"},"type":"statement","id":"Q104444$85922E4B-51EF-41E9-8A21-65CB48B07297","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"4af3404238482b8faea04abf62db0a8e08bd1c4c","datavalue":{"value":"CID11:ID_1148757980","type":"string"},"datatype":"string"},"type":"statement","id":"Q104444$4987E39B-B513-4E00-ACEF-D4877B83EC3F","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"93f9e4c6490cadbb9cce8eeebd6632d96908c969","datavalue":{"value":"dki-india-ID_1148757980","type":"string"},"datatype":"string"},"type":"statement","id":"Q104444$9E3731DC-AF97-4F1E-940B-758E30CCBC7B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q104444$9566DC24-489B-41C9-8A63-8F31E9D5F442","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q104444$62279154-7B7A-4251-A5FD-716CA35AB72E","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q104444$13C0E147-1239-483A-9202-01C7161C562A","rank":"normal"}]},"sitelinks":{}}}}