Diffuse cutaneous mastocytosis (Q94594): Difference between revisions
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Mastocitose cutânea difusa é uma forma rara de mastocitose cutânea na qual os mastócitos se infiltram em toda a pele de forma difusa. Geralmente se apresenta no período neonatal e é caracterizada por eritrodermia, uma aparência pastosa de "peau d'orange" e aparecimento te bolhas após pequenos traumatismos. Os bebês afetados estão em risco para doença sistêmica e complicações graves, incluindo anafilaxia e diarreia. A condição pode se resolver espontaneamente. | |||
| description / en | description / en | ||
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously. | |||
Revision as of 09:52, 16 August 2026
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_193128939 |
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| English | Diffuse cutaneous mastocytosis |
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously. |
