Haemophilia B (Q39577): Difference between revisions
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Hemofilia B é uma forma de hemofilia caracterizada pela ocorrência de hemorragias espontâneas ou prolongadas devido à deficiência do fator IX. A depender da intensidade da deficiência do fator IX, pode ser grave (atividade biológica do fator IX inferior a 1%), moderadamente grave (atividade biológica do fator IX entre 1% e 5%), ou leve (atividade biológica do fator IX entre 5% e 40%). | |||
| description / en | description / en | ||
Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor IX deficiency. Depending on the extent of the factor IX deficiency, it can be severe (biological activity of factor IX below 1%), moderately severe (activity of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%). | |||
Revision as of 05:03, 13 August 2026
Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor IX deficiency. Depending on the extent of the factor IX deficiency, it can be severe (biological activity of factor IX below 1%), moderately severe (activity of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%).
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 3B11.0 |
||
| English | Haemophilia B |
Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor IX deficiency. Depending on the extent of the factor IX deficiency, it can be severe (biological activity of factor IX below 1%), moderately severe (activity of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%). |
