Dilated cardiomyopathy due to iron overload (Q98625): Difference between revisions

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Cardiomiopatia dilatada devida a sobrecarga de ferro ocorre ou primariamente devido a uma predisposição genética para absorver e armazenar ferro em quantidades excessivas (hemocromatose hereditária) ou secundariamente como uma complicação de outros transtornos hematológicos que requerem terapia de transfusão crônica (como doença falciforme e talassemia), injeções repetidas de ferro parenteral (como para doença renal crônica), ou devido a ingestão excessiva de ferro._x000D_ _x000D_ Informações adicionais: A cardiomiopatia por sobrecarga de ferro em crianças e adultos jovens com as condições acima começa como uma cardiomiopatia restritiva com disfunção diastólica grave, eventualmente progredindo para cardiomiopatia dilatada em estágio terminal com disfunção sistólica e diastólica mista.
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Dilated cardiomyopathy due to iron overload occurs either primarily due to a genetic predisposition to absorb and store iron in excess amounts (hereditary haemochromatosis), or secondarily as a complication of other haematologic disorders that require chronic transfusion therapy (such as sickle cell disease and thalassaemia), repeated injections of parenteral iron (such as for chronic kidney disease), or due to excessive iron ingestion. Additional information: Iron-overload cardiomyopathy in children and young adults with the above conditions begins as a restrictive cardiomyopathy with severe diastolic dysfunction, eventually progressing to end-stage dilated cardiomyopathy with mixed systolic and diastolic dysfunction.
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Property / Canonical URI: https://id.who.int/icd/entity/808521772 / rank
 
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CID11:ID_808521772
Property / CURIE: CID11:ID_808521772 / rank
 
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dki-india-ID_808521772
Property / Canary Token: dki-india-ID_808521772 / rank
 
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Concluído
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Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank
 
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15 August 2026
Timestamp+2026-08-15T00:00:00Z
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CalendarGregorian
Precision1 day
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Property / Collection date: 15 August 2026 / rank
 
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Latest revision as of 15:11, 16 August 2026

Dilated cardiomyopathy due to iron overload occurs either primarily due to a genetic predisposition to absorb and store iron in excess amounts (hereditary haemochromatosis), or secondarily as a complication of other haematologic disorders that require chronic transfusion therapy (such as sickle cell disease and thalassaemia), repeated injections of parenteral iron (such as for chronic kidney disease), or due to excessive iron ingestion. Additional information: Iron-overload cardiomyopathy in children and young adults with the above conditions begins as a restrictive cardiomyopathy with severe diastolic dysfunction, eventually progressing to end-stage dilated cardiomyopathy with mixed systolic and diastolic dysfunction.
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ID_808521772
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    Dilated cardiomyopathy due to iron overload
    Dilated cardiomyopathy due to iron overload occurs either primarily due to a genetic predisposition to absorb and store iron in excess amounts (hereditary haemochromatosis), or secondarily as a complication of other haematologic disorders that require chronic transfusion therapy (such as sickle cell disease and thalassaemia), repeated injections of parenteral iron (such as for chronic kidney disease), or due to excessive iron ingestion. Additional information: Iron-overload cardiomyopathy in children and young adults with the above conditions begins as a restrictive cardiomyopathy with severe diastolic dysfunction, eventually progressing to end-stage dilated cardiomyopathy with mixed systolic and diastolic dysfunction.

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      CID11:ID_808521772
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      dki-india-ID_808521772
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      Concluído
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      15 August 2026
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