Diffuse cutaneous mastocytosis (Q94594): Difference between revisions
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Mastocitose cutânea difusa é uma forma rara de mastocitose cutânea na qual os mastócitos se infiltram em toda a pele de forma difusa. Geralmente se apresenta no período neonatal e é caracterizada por eritrodermia, uma aparência pastosa de "peau d'orange" e aparecimento te bolhas após pequenos traumatismos. Os bebês afetados estão em risco para doença sistêmica e complicações graves, incluindo anafilaxia e diarreia. A condição pode se resolver espontaneamente. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/193128939 / rank | |||||||||||||||
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CID11:ID_193128939 | |||||||||||||||
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dki-india-ID_193128939 | |||||||||||||||
| Property / Canary Token: dki-india-ID_193128939 / rank | |||||||||||||||
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| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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15 August 2026
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| Property / Collection date: 15 August 2026 / rank | |||||||||||||||
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Latest revision as of 09:52, 16 August 2026
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_193128939 |
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| English | Diffuse cutaneous mastocytosis |
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast cells infiltrate the entire skin diffusely. It usually presents in the neonatal period and is characterised by erythroderma, a doughy ''peau d'orange'' appearance and blistering after minor trauma. Affected infants are at risk of systemic disease and severe complications including anaphylaxis and diarrhoea. The condition may resolve spontaneously. |
Statements
CID11:ID_193128939
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dki-india-ID_193128939
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Concluído
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15 August 2026
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