Primary cutaneous gamma/delta T-cell lymphoma (Q89578): Difference between revisions
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Linfoma cutâneo agressivo de linfócitos T gama/delta maduros ativados. Geralmente se apresenta com placas e nódulos disseminados. O envolvimento de mucosas é frequente. No entanto, o envolvimento de linfonodos, baço ou medula óssea é incomum. Morfologicamente, existem três padrões de envolvimento cutâneo: epidermotrópico, dérmico e subcutâneo. Freqüentemente, mais de um padrão podem coexistir em uma única amostra de biópsia ou podem estar presente em diferentes amostras de biópsia do mesmo paciente. O infiltrado linfocítico é composto por linfócitos de médio a grande porte que expressam CD56. A maioria dos casos não expressa CD4 e CD8, embora CD8 possa estar presente em alguns casos. Este grupo de linfomas inclui casos anteriormente conhecidos como linfoma de células T tipo paniculite subcutâneo com fenótipo gama/delta. | |||||||||||||||
| description / en | description / en | ||||||||||||||
An aggressive cutaneous lymphoma of mature, activated gamma/delta T-lymphocytes. It usually presents with disseminated plaques and nodules. Involvement of mucosal sites is frequent. However, involvement of lymph nodes, spleen, or bone marrow is uncommon. Morphologically, there are three patterns of cutaneous involvement: epidermotropic, dermal, and subcutaneous. Often, more than one pattern may co-exist in a single biopsy specimen, or may be present in different biopsy specimens from the same patient. The lymphocytic infiltrate is composed of medium- to large-sized lymphocytes expressing CD56. Most cases lack both CD4 and CD8, although CD8 may be present in some cases. This group of lymphomas includes cases previously known as subcutaneous panniculitis-like T-cell lymphoma with a gamma/delta phenotype. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/1158873778 / rank | |||||||||||||||
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CID11:ID_1158873778 | |||||||||||||||
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dki-india-ID_1158873778 | |||||||||||||||
| Property / Canary Token: dki-india-ID_1158873778 / rank | |||||||||||||||
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Concluído | |||||||||||||||
| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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Latest revision as of 16:23, 15 August 2026
An aggressive cutaneous lymphoma of mature, activated gamma/delta T-lymphocytes. It usually presents with disseminated plaques and nodules. Involvement of mucosal sites is frequent. However, involvement of lymph nodes, spleen, or bone marrow is uncommon. Morphologically, there are three patterns of cutaneous involvement: epidermotropic, dermal, and subcutaneous. Often, more than one pattern may co-exist in a single biopsy specimen, or may be present in different biopsy specimens from the same patient. The lymphocytic infiltrate is composed of medium- to large-sized lymphocytes expressing CD56. Most cases lack both CD4 and CD8, although CD8 may be present in some cases. This group of lymphomas includes cases previously known as subcutaneous panniculitis-like T-cell lymphoma with a gamma/delta phenotype.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1158873778 |
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| English | Primary cutaneous gamma/delta T-cell lymphoma |
An aggressive cutaneous lymphoma of mature, activated gamma/delta T-lymphocytes. It usually presents with disseminated plaques and nodules. Involvement of mucosal sites is frequent. However, involvement of lymph nodes, spleen, or bone marrow is uncommon. Morphologically, there are three patterns of cutaneous involvement: epidermotropic, dermal, and subcutaneous. Often, more than one pattern may co-exist in a single biopsy specimen, or may be present in different biopsy specimens from the same patient. The lymphocytic infiltrate is composed of medium- to large-sized lymphocytes expressing CD56. Most cases lack both CD4 and CD8, although CD8 may be present in some cases. This group of lymphomas includes cases previously known as subcutaneous panniculitis-like T-cell lymphoma with a gamma/delta phenotype. |
Statements
CID11:ID_1158873778
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dki-india-ID_1158873778
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Concluído
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13 August 2026
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