{"entities":{"Q89578":{"pageid":79964,"ns":120,"title":"Item:Q89578","lastrevid":494913,"modified":"2026-08-15T16:23:28Z","type":"item","id":"Q89578","labels":{"mul":{"language":"mul","value":"ID_1158873778"},"pt-br":{"language":"pt-br","value":"Linfoma cut\u00e2neo prim\u00e1rio de c\u00e9lulas T gama-delta"},"en":{"language":"en","value":"Primary cutaneous gamma/delta T-cell lymphoma"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Linfoma cut\u00e2neo agressivo de linf\u00f3citos T gama/delta maduros ativados. Geralmente se apresenta com placas e n\u00f3dulos disseminados. O envolvimento de mucosas \u00e9 frequente. No entanto, o envolvimento de linfonodos, ba\u00e7o ou medula \u00f3ssea \u00e9 incomum. Morfologicamente, existem tr\u00eas padr\u00f5es de envolvimento cut\u00e2neo: epidermotr\u00f3pico, d\u00e9rmico e subcut\u00e2neo. Freq\u00fcentemente, mais de um padr\u00e3o podem coexistir em uma \u00fanica amostra de bi\u00f3psia ou podem estar presente em diferentes amostras de bi\u00f3psia do mesmo paciente. O infiltrado linfoc\u00edtico \u00e9 composto por linf\u00f3citos de m\u00e9dio a grande porte que expressam CD56. A maioria dos casos n\u00e3o expressa CD4 e CD8, embora CD8 possa estar presente em alguns casos. Este grupo de linfomas inclui casos anteriormente conhecidos como linfoma de c\u00e9lulas T tipo paniculite subcut\u00e2neo com fen\u00f3tipo gama/delta."},"en":{"language":"en","value":"An aggressive cutaneous lymphoma of mature, activated gamma/delta T-lymphocytes. It usually presents with disseminated plaques and nodules. Involvement of mucosal sites is frequent. However, involvement of lymph nodes, spleen, or bone marrow is uncommon. Morphologically, there are three patterns of cutaneous involvement: epidermotropic, dermal, and subcutaneous. Often, more than one pattern may co-exist in a single biopsy specimen, or may be present in different biopsy specimens from the same patient. The lymphocytic infiltrate is composed of medium- to large-sized lymphocytes expressing CD56. Most cases lack both CD4 and CD8, although CD8 may be present in some cases. This group of lymphomas includes cases previously known as subcutaneous panniculitis-like T-cell lymphoma with a gamma/delta phenotype."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"b26e9325f0fe662eacd6fe2db86d34c763ce4f79","datavalue":{"value":"https://id.who.int/icd/entity/1158873778","type":"string"},"datatype":"url"},"type":"statement","id":"Q89578$CA715ED5-65FA-4741-A631-DF939C2D9D63","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"51ca470c2405592ad22f8bfefbbd8a750183a58e","datavalue":{"value":"CID11:ID_1158873778","type":"string"},"datatype":"string"},"type":"statement","id":"Q89578$B1823F4D-00C2-49DD-B127-096DAECE8322","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"9bd60d65f2a3864fe257eb170be4762b634f3e09","datavalue":{"value":"dki-india-ID_1158873778","type":"string"},"datatype":"string"},"type":"statement","id":"Q89578$2F1CDDFD-5ECF-4405-8A4C-3CE300D7270B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q89578$AAFF5534-3089-433C-A900-A055CFC48AEF","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q89578$1336779A-015D-4018-A155-16983B5DC0FF","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q89578$87C352F3-23C0-4E6D-8375-C3F06017C0BB","rank":"normal"}]},"sitelinks":{}}}}