Primary cutaneous plasmacytosis (Q44400): Difference between revisions
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Transtorno cutâneo resultante da infiltração densa focal ou multifocal da pele por agregados de plasmócitos. Pode estar associada a níveis elevados de IgG4 no soro. Tipicamente se apresenta como pápulas vermelho-amarronzadas disseminadas, nódulos e placas pigmentadas enduradas envolvendo tronco e membros, mas pode se apresentar como um único nódulo ou placa. A maioria dos pacientes com este transtorno de pele incomum são descendentes do leste asiático. Existe um risco de progressão para malignidade linfoproliferativa sistêmica. | |||||||||||||||
| description / en | description / en | ||||||||||||||
A skin disorder resulting from focal or multifocal dense infiltration of the skin by plasma cell aggregates. It may be associated with high levels of serum IgG4. It typically presents as widespread reddish-brown papules, nodules and pigmented indurated plaques involving the trunk and limbs but may present as a single nodule or plaque. The majority of patients with this uncommon skin disorder are of East Asian descent. There is a risk of progression to systemic lymphoproliferative malignancy. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/1669369613 / rank | |||||||||||||||
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CID11:EK91.2 | |||||||||||||||
| Property / CURIE: CID11:EK91.2 / rank | |||||||||||||||
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dki-india-EK91.2 | |||||||||||||||
| Property / Canary Token: dki-india-EK91.2 / rank | |||||||||||||||
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Concluído | |||||||||||||||
| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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| Property / Linked ICD 10: M35.8 / rank | |||||||||||||||
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Latest revision as of 11:51, 13 August 2026
A skin disorder resulting from focal or multifocal dense infiltration of the skin by plasma cell aggregates. It may be associated with high levels of serum IgG4. It typically presents as widespread reddish-brown papules, nodules and pigmented indurated plaques involving the trunk and limbs but may present as a single nodule or plaque. The majority of patients with this uncommon skin disorder are of East Asian descent. There is a risk of progression to systemic lymphoproliferative malignancy.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | EK91.2 |
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| English | Primary cutaneous plasmacytosis |
A skin disorder resulting from focal or multifocal dense infiltration of the skin by plasma cell aggregates. It may be associated with high levels of serum IgG4. It typically presents as widespread reddish-brown papules, nodules and pigmented indurated plaques involving the trunk and limbs but may present as a single nodule or plaque. The majority of patients with this uncommon skin disorder are of East Asian descent. There is a risk of progression to systemic lymphoproliferative malignancy. |
Statements
CID11:EK91.2
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dki-india-EK91.2
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Concluído
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13 August 2026
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