{"entities":{"Q44400":{"pageid":34768,"ns":120,"title":"Item:Q44400","lastrevid":163330,"modified":"2026-08-13T11:51:19Z","type":"item","id":"Q44400","labels":{"mul":{"language":"mul","value":"EK91.2"},"pt-br":{"language":"pt-br","value":"Plasmocitose cut\u00e2nea prim\u00e1ria"},"en":{"language":"en","value":"Primary cutaneous plasmacytosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Transtorno cut\u00e2neo resultante da infiltra\u00e7\u00e3o densa focal ou multifocal da pele por agregados de plasm\u00f3citos. Pode estar associada a n\u00edveis elevados de IgG4 no soro. Tipicamente se apresenta como p\u00e1pulas vermelho-amarronzadas disseminadas, n\u00f3dulos e placas pigmentadas enduradas envolvendo tronco e membros, mas pode se apresentar como um \u00fanico n\u00f3dulo ou placa. A maioria dos pacientes com este transtorno de pele incomum s\u00e3o descendentes do leste asi\u00e1tico. Existe um risco de progress\u00e3o para malignidade linfoproliferativa sist\u00eamica."},"en":{"language":"en","value":"A skin disorder resulting from focal or multifocal dense infiltration of the skin by plasma cell aggregates. It may be associated with high levels of serum IgG4. It typically presents as widespread reddish-brown papules, nodules and pigmented indurated plaques involving the trunk and limbs but may present as a single nodule or plaque. The majority of patients with this uncommon skin disorder are of East Asian descent. There is a risk of progression to systemic lymphoproliferative malignancy."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"fabafc9f26fa96457c64c479bf223dbf8519e667","datavalue":{"value":"https://id.who.int/icd/entity/1669369613","type":"string"},"datatype":"url"},"type":"statement","id":"Q44400$757B119B-7E70-4D6B-9CBB-C8BA9CA46A0F","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"e1cbedd3359f21f18898f3dd52d906964117b32c","datavalue":{"value":"CID11:EK91.2","type":"string"},"datatype":"string"},"type":"statement","id":"Q44400$9EF5A81C-AD0A-4833-87E5-6622F0355A70","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"dbf4aed7bca9a11f75ec6d62f67828bca0c52fde","datavalue":{"value":"dki-india-EK91.2","type":"string"},"datatype":"string"},"type":"statement","id":"Q44400$DA21317A-D78A-4C26-924B-2DDAB25D5952","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q44400$998A2629-4E38-4B4C-BCE4-419D57269AED","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q44400$31BD4CF9-6884-48FA-BF3D-CC487707FD1A","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q44400$EFE05CE9-3402-447B-BBA0-C6840506770E","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"fff8dac24a12980e82ff275d51f444a6717afacd","datavalue":{"value":{"entity-type":"item","numeric-id":19949,"id":"Q19949"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q44400$FF365CD9-CD5F-4FA7-B206-20C35EE2D53C","rank":"normal"}]},"sitelinks":{}}}}