Juvenile dermatomyositis with necrotising cutaneous vasculitis (Q92493): Difference between revisions

@@ description / pt-br / description / pt-br @@
+Tipo de miopatia inflamatória idiopática caracterizada por erupção cutânea acompanhada de fraqueza muscular, anorexia e fadiga. A forma juvenil apresenta-se de maneira mais insidiosa com fraqueza muscular, particularmente dos flexores do pescoço, frequentemente precedida por fadiga e febre baixa. Associado a erupção heliotrópica, eritema periorbitário, pápulas de Gottron sobre a face extensora das articulações metacarpofalângicas e interfalângicas, cotovelos e joelhos e telangectasias periungueais. A forma juvenil está associada a maior envolvimento de vasos sanguíneos e vasculopatia em comparação com a forma do adulto.
@@ description / en / description / en @@
+Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form.
@@ Property / Canonical URI @@
+https://id.who.int/icd/entity/504741085
@@ Property / Canonical URI: https://id.who.int/icd/entity/504741085 / rank @@
+Normal rank
@@ Property / CURIE @@
+CID11:ID_504741085
@@ Property / CURIE: CID11:ID_504741085 / rank @@
+Normal rank
@@ Property / Canary Token @@
+dki-india-ID_504741085
@@ Property / Canary Token: dki-india-ID_504741085 / rank @@
+Normal rank
@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
+Normal rank
@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-15T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-15T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 15 August 2026 / rank @@
+Normal rank

Latest revision as of 07:37, 16 August 2026

Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form.

Language	Label	Description	Also known as
default for all languages	ID_504741085
English	Juvenile dermatomyositis with necrotising cutaneous vasculitis	Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form.