Pulmonary atresia with intact ventricular septum (Q46177): Difference between revisions

@@ description / pt-br / description / pt-br @@
+Malformação cardiovascular congênita em que normalmente existem grandes artérias alinhadas, nenhuma abertura entre o ventrículo morfologicamente direito e o tronco pulmonar e nenhuma comunicação no nível ventricular._x000D_ _x000D_ Informações adicionais: atresia pulmonar com septo ventricular íntegro é uma malformação congênita dependente do ducto que forma um espectro de lesões incluindo atresia da valva pulmonar, um grau variável de hipoplasia do ventrículo direito e da valva tricúspide e anomalias da circulação coronária. Uma circulação arterial coronária dependente do ventrículo direito está presente quando as fístulas da artéria coronária estão associadas a uma estenose proximal de artéria coronária. Anomalia de Ebstein associada da valva tricúspide pode estar presente.
@@ description / en / description / en @@
+A congenital cardiovascular malformation in which there are normally aligned great arteries, no opening between the morphologically right ventricle and the pulmonary trunk, and no ventricular level communication. Additional information: pulmonary atresia with intact ventricular septum is a duct-dependent congenital malformation that forms a spectrum of lesions including atresia of the pulmonary valve, a varying degree of right ventricle and tricuspid valve hypoplasia, and anomalies of the coronary circulation. A right ventricular dependent coronary artery circulation is present when coronary artery fistulas are associated with a proximal coronary artery stenosis. Associated Ebstein anomaly of the tricuspid valve can be present.
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+https://id.who.int/icd/entity/131289265
@@ Property / Canonical URI: https://id.who.int/icd/entity/131289265 / rank @@
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+CID11:LA8A.10
@@ Property / CURIE: CID11:LA8A.10 / rank @@
+Normal rank
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+dki-india-LA8A.10
@@ Property / Canary Token: dki-india-LA8A.10 / rank @@
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@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
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@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-13T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-13T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 13 August 2026 / rank @@
+Normal rank
@@ Property / Linked ICD 10 @@
+Q22.0
@@ Property / Linked ICD 10: Q22.0 / rank @@
+Normal rank

Latest revision as of 14:35, 13 August 2026

A congenital cardiovascular malformation in which there are normally aligned great arteries, no opening between the morphologically right ventricle and the pulmonary trunk, and no ventricular level communication. Additional information: pulmonary atresia with intact ventricular septum is a duct-dependent congenital malformation that forms a spectrum of lesions including atresia of the pulmonary valve, a varying degree of right ventricle and tricuspid valve hypoplasia, and anomalies of the coronary circulation. A right ventricular dependent coronary artery circulation is present when coronary artery fistulas are associated with a proximal coronary artery stenosis. Associated Ebstein anomaly of the tricuspid valve can be present.

Language	Label	Description	Also known as
default for all languages	LA8A.10
English	Pulmonary atresia with intact ventricular septum	A congenital cardiovascular malformation in which there are normally aligned great arteries, no opening between the morphologically right ventricle and the pulmonary trunk, and no ventricular level communication. Additional information: pulmonary atresia with intact ventricular septum is a duct-dependent congenital malformation that forms a spectrum of lesions including atresia of the pulmonary valve, a varying degree of right ventricle and tricuspid valve hypoplasia, and anomalies of the coronary circulation. A right ventricular dependent coronary artery circulation is present when coronary artery fistulas are associated with a proximal coronary artery stenosis. Associated Ebstein anomaly of the tricuspid valve can be present.