{"entities":{"Q46177":{"pageid":36548,"ns":120,"title":"Item:Q46177","lastrevid":178764,"modified":"2026-08-13T14:35:19Z","type":"item","id":"Q46177","labels":{"mul":{"language":"mul","value":"LA8A.10"},"pt-br":{"language":"pt-br","value":"Atresia pulmonar com septo ventricular intacto"},"en":{"language":"en","value":"Pulmonary atresia with intact ventricular septum"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Malforma\u00e7\u00e3o cardiovascular cong\u00eanita em que normalmente existem grandes art\u00e9rias alinhadas, nenhuma abertura entre o ventr\u00edculo morfologicamente direito e o tronco pulmonar e nenhuma comunica\u00e7\u00e3o no n\u00edvel ventricular._x000D_ _x000D_ Informa\u00e7\u00f5es adicionais: atresia pulmonar com septo ventricular \u00edntegro \u00e9 uma malforma\u00e7\u00e3o cong\u00eanita dependente do ducto que forma um espectro de les\u00f5es incluindo atresia da valva pulmonar, um grau vari\u00e1vel de hipoplasia do ventr\u00edculo direito e da valva tric\u00faspide e anomalias da circula\u00e7\u00e3o coron\u00e1ria. Uma circula\u00e7\u00e3o arterial coron\u00e1ria dependente do ventr\u00edculo direito est\u00e1 presente quando as f\u00edstulas da art\u00e9ria coron\u00e1ria est\u00e3o associadas a uma estenose proximal de art\u00e9ria coron\u00e1ria. Anomalia de Ebstein associada da valva tric\u00faspide pode estar presente."},"en":{"language":"en","value":"A congenital cardiovascular malformation in which there are normally aligned great arteries, no opening between the morphologically right ventricle and the pulmonary trunk, and no ventricular level communication. Additional information: pulmonary atresia with intact ventricular septum is a duct-dependent congenital malformation that forms a spectrum of lesions including atresia of the pulmonary valve, a varying degree of right ventricle and tricuspid valve hypoplasia, and anomalies of the coronary circulation. A right ventricular dependent coronary artery circulation is present when coronary artery fistulas are associated with a proximal coronary artery stenosis. Associated Ebstein anomaly of the tricuspid valve can be present."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"9a03c78fe7d35ac308024165c14a8bbeb7107e05","datavalue":{"value":"https://id.who.int/icd/entity/131289265","type":"string"},"datatype":"url"},"type":"statement","id":"Q46177$6A93DB94-8786-41E2-A7F6-AFB285E2E67C","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"1f30dbf2a7dd703d0827a66077da903dba7176b9","datavalue":{"value":"CID11:LA8A.10","type":"string"},"datatype":"string"},"type":"statement","id":"Q46177$CA17FB62-DCE6-4331-AF8E-8755AB3E8D5B","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"be83c04dd5da7daea38239dde82e83d4664c4e07","datavalue":{"value":"dki-india-LA8A.10","type":"string"},"datatype":"string"},"type":"statement","id":"Q46177$29F4D36E-DC72-4459-AEC2-91950EE8F89B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46177$05AAEE15-B054-40CE-B7CC-2DE8FEDFDA58","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46177$D0949C47-CE4F-4E3E-84DB-D27B6E695C6D","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46177$9DEEDAB5-3D7D-4EE2-9A7B-BB62253D3A5B","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"ae90498838a4daad17c6a369b79c684e2c1f2bd4","datavalue":{"value":{"entity-type":"item","numeric-id":220,"id":"Q220"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46177$69D5EBED-F691-4042-8847-1EEDBD877DA0","rank":"normal"}]},"sitelinks":{}}}}