Autoimmune retinopathy (Q41748): Difference between revisions
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As retinopatias autoimunes são doenças inflamatórias imunomediadas da retina que diferem das retinopatias paraneoplásicas pela falta de associação com o câncer. Os pacientes apresentam perda visual progressiva e disfunção de bastonetes (dificuldade de adaptação ao escuro e problemas de visão periférica) e de cones (acuidade visual, disfunção de cor, fotossensibilidade e ofuscamento). Os sintomas costumam ser piores do que os sinais clínicos na fundoscopia. Múltiplos autoanticorpos anti-retinianos (p. ex., anticorpos anti-recoverina) são descritos, embora seu significado seja incerto. A retinopatia autoimune é um diagnóstico de exclusão e outras causas de retinopatia precisam ser descartadas, enquanto o papel potencial da imunoterapia permanece incerto._x000D_ _x000D_ Os autoanticorpos neurais associados incluem:_x000D_ autoanticorpos anti-recoverina; autoanticorpos alfa-enolase; autoanticorpos anti-transducina; | |||||||||||||||
| description / en | description / en | ||||||||||||||
Autoimmune retinopathies are immune-mediated inflammatory disorders of the retina that differ from paraneoplastic retinopathies in the lack of association with cancer. Patients present with progressive visual loss and dysfunction of rods (impaired dark adaption and peripheral vision problems) and cones (visual acuity, colour dysfunction, photosensitivity and glare) may occur. The symptoms are often worse than the clinical signs on fundoscopy. Multiple anti-retinal autoantibodies (e.g. anti-recoverin antibodies) are described although their significance is uncertain. Autoimmune retinopathy is a diagnosis of exclusion and other causes of retinopathy need to be ruled out, while the potential role of immunotherapy remains uncertain. Associated neural autoantibodies include: anti-recoverin autoantibodies; alpha-enolase autoantibodies; anti-transducin autoantibodies. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/1969888129 / rank | |||||||||||||||
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CID11:9B71.5 | |||||||||||||||
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dki-india-9B71.5 | |||||||||||||||
| Property / Canary Token: dki-india-9B71.5 / rank | |||||||||||||||
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| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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| Property / Linked ICD 10: H30-H36 / rank | |||||||||||||||
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Latest revision as of 08:01, 13 August 2026
Autoimmune retinopathies are immune-mediated inflammatory disorders of the retina that differ from paraneoplastic retinopathies in the lack of association with cancer. Patients present with progressive visual loss and dysfunction of rods (impaired dark adaption and peripheral vision problems) and cones (visual acuity, colour dysfunction, photosensitivity and glare) may occur. The symptoms are often worse than the clinical signs on fundoscopy. Multiple anti-retinal autoantibodies (e.g. anti-recoverin antibodies) are described although their significance is uncertain. Autoimmune retinopathy is a diagnosis of exclusion and other causes of retinopathy need to be ruled out, while the potential role of immunotherapy remains uncertain. Associated neural autoantibodies include: anti-recoverin autoantibodies; alpha-enolase autoantibodies; anti-transducin autoantibodies.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 9B71.5 |
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| English | Autoimmune retinopathy |
Autoimmune retinopathies are immune-mediated inflammatory disorders of the retina that differ from paraneoplastic retinopathies in the lack of association with cancer. Patients present with progressive visual loss and dysfunction of rods (impaired dark adaption and peripheral vision problems) and cones (visual acuity, colour dysfunction, photosensitivity and glare) may occur. The symptoms are often worse than the clinical signs on fundoscopy. Multiple anti-retinal autoantibodies (e.g. anti-recoverin antibodies) are described although their significance is uncertain. Autoimmune retinopathy is a diagnosis of exclusion and other causes of retinopathy need to be ruled out, while the potential role of immunotherapy remains uncertain. Associated neural autoantibodies include: anti-recoverin autoantibodies; alpha-enolase autoantibodies; anti-transducin autoantibodies. |
Statements
CID11:9B71.5
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dki-india-9B71.5
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Concluído
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13 August 2026
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