{"entities":{"Q41748":{"pageid":32116,"ns":120,"title":"Item:Q41748","lastrevid":140735,"modified":"2026-08-13T08:01:20Z","type":"item","id":"Q41748","labels":{"mul":{"language":"mul","value":"9B71.5"},"pt-br":{"language":"pt-br","value":"Retinopatia autoimune"},"en":{"language":"en","value":"Autoimmune retinopathy"}},"descriptions":{"pt-br":{"language":"pt-br","value":"As retinopatias autoimunes s\u00e3o doen\u00e7as inflamat\u00f3rias imunomediadas da retina que diferem das retinopatias paraneopl\u00e1sicas pela falta de associa\u00e7\u00e3o com o c\u00e2ncer. Os pacientes apresentam perda visual progressiva e disfun\u00e7\u00e3o de bastonetes (dificuldade de adapta\u00e7\u00e3o ao escuro e problemas de vis\u00e3o perif\u00e9rica) e de cones (acuidade visual, disfun\u00e7\u00e3o de cor, fotossensibilidade e ofuscamento). Os sintomas costumam ser piores do que os sinais cl\u00ednicos na fundoscopia. M\u00faltiplos autoanticorpos anti-retinianos (p. ex., anticorpos anti-recoverina) s\u00e3o descritos, embora seu significado seja incerto. A retinopatia autoimune \u00e9 um diagn\u00f3stico de exclus\u00e3o e outras causas de retinopatia precisam ser descartadas, enquanto o papel potencial da imunoterapia permanece incerto._x000D_ _x000D_ Os autoanticorpos neurais associados incluem:_x000D_ autoanticorpos anti-recoverina; autoanticorpos alfa-enolase; autoanticorpos anti-transducina;"},"en":{"language":"en","value":"Autoimmune retinopathies are immune-mediated inflammatory disorders of the retina that differ from paraneoplastic retinopathies in the lack of association with cancer. Patients present with progressive visual loss and dysfunction of rods (impaired dark adaption and peripheral vision problems) and cones (visual acuity, colour dysfunction, photosensitivity and glare) may occur. The symptoms are often worse than the clinical signs on fundoscopy. Multiple anti-retinal autoantibodies (e.g. anti-recoverin antibodies) are described although their significance is uncertain. Autoimmune retinopathy is a diagnosis of exclusion and other causes of retinopathy need to be ruled out, while the potential role of immunotherapy remains uncertain.  Associated neural autoantibodies include: anti-recoverin autoantibodies; alpha-enolase autoantibodies; anti-transducin autoantibodies."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"a57efd6ecfd228e0de691ff850f85d276bb8b55d","datavalue":{"value":"https://id.who.int/icd/entity/1969888129","type":"string"},"datatype":"url"},"type":"statement","id":"Q41748$659669D3-3453-427D-9557-A1D76125709A","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"40e9c1cec291a2d464d3b68e5cd0fc8067be09d4","datavalue":{"value":"CID11:9B71.5","type":"string"},"datatype":"string"},"type":"statement","id":"Q41748$F0269234-72E6-4BFB-B003-073B508F397E","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"a8f432ba0ad3f73f97e7c1a11ae6a9d11a84476c","datavalue":{"value":"dki-india-9B71.5","type":"string"},"datatype":"string"},"type":"statement","id":"Q41748$FD57D2F5-2BFB-4B8E-AA08-869A1C4FDC09","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41748$2D26B0C2-135D-4836-81D9-B2B1EF53CBB2","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41748$FA29B5C3-E986-4F3B-8F72-653F5C9E5023","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41748$54A74938-0B66-4797-9B5E-D0DACA6A9C97","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"5b66d5bb7bf4ceb4d2306d3766ba7f0cecf6aaab","datavalue":{"value":{"entity-type":"item","numeric-id":41719,"id":"Q41719"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41748$D3FC1E4F-D143-4E93-BBF4-D7C6EDDB5F4E","rank":"normal"}]},"sitelinks":{}}}}