{"entities":{"Q98288":{"pageid":88681,"ns":120,"title":"Item:Q98288","lastrevid":557469,"modified":"2026-08-16T14:41:09Z","type":"item","id":"Q98288","labels":{"mul":{"language":"mul","value":"ID_2089325724"},"pt-br":{"language":"pt-br","value":"Hialinose sist\u00eamica infantil"},"en":{"language":"en","value":"Infantile systemic hyalinosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A hialinose sist\u00eamica infantil \u00e9 uma doen\u00e7a muito rara pertencente ao grupo heterog\u00eaneo das fibromatoses gen\u00e9ticas e \u00e9 caracterizada por contraturas articulares progressivas, anormalidades da pele, dor cr\u00f4nica intensa e deposi\u00e7\u00e3o generalizada de material hialino em muitos tecidos, como pele, m\u00fasculo esquel\u00e9tico, m\u00fasculo card\u00edaco, trato gastrointestinal, n\u00f3dulos linf\u00e1ticos, ba\u00e7o, tireoide e gl\u00e2ndulas suprarrenais."},"en":{"language":"en","value":"Infantile systemic hyalinosis is a very rare disorder belonging to the heterogeneous group of genetic fibromatoses and is characterised by progressive joint contractures, skin abnormalities, severe chronic pain and widespread deposition of hyaline material in many tissues such as the skin, skeletal muscle, cardiac muscle, gastrointestinal tract, lymph nodes, spleen, thyroid, and adrenal glands."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"d940042d6bd279bc44d970a4baf4fb4d59776b20","datavalue":{"value":"https://id.who.int/icd/entity/2089325724","type":"string"},"datatype":"url"},"type":"statement","id":"Q98288$EF72D983-4BDC-45FF-8AC8-162A80B08BEA","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"11ba969b4ef198cd560b06d876a79f15246746ca","datavalue":{"value":"CID11:ID_2089325724","type":"string"},"datatype":"string"},"type":"statement","id":"Q98288$1E03ADFF-61CD-4DB1-A3A7-6C81ECE881A3","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"1532f192fabce296104f0357d0c2904d83f827af","datavalue":{"value":"dki-india-ID_2089325724","type":"string"},"datatype":"string"},"type":"statement","id":"Q98288$A1BB5E9C-6CA8-440A-A8F4-8C4B946ABD12","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q98288$ECF02D19-2727-446F-A2C9-F986E919BF00","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q98288$D1BCEA72-6D32-4863-8285-9AB9AC7F83C4","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q98288$A908C65D-187A-4AE1-B23A-C82F8E3D59CC","rank":"normal"}]},"sitelinks":{}}}}