{"entities":{"Q97536":{"pageid":87929,"ns":120,"title":"Item:Q97536","lastrevid":552043,"modified":"2026-08-16T13:39:09Z","type":"item","id":"Q97536","labels":{"mul":{"language":"mul","value":"ID_1541297428"},"pt-br":{"language":"pt-br","value":"Hemocromatose heredit\u00e1ria n\u00e3o relacionada ao HFE, tipo 4"},"en":{"language":"en","value":"Non-HFE-related hereditary haemochromatosis, Type 4"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A hemocromatose tipo 4 (tamb\u00e9m chamada de doen\u00e7a da ferroportina) \u00e9 uma forma rara de hemocromatose heredit\u00e1ria, um grupo de doen\u00e7as de origem gen\u00e9tica caracterizadas pela deposi\u00e7\u00e3o excessiva de ferro nos tecidos. \u00c9 fenotipicamente heterog\u00eanea com dois subtipos. A forma A da doen\u00e7a da ferroportina \u00e9 a forma usual e geralmente assintom\u00e1tica, sem danos aos tecidos e outras complica\u00e7\u00f5es. A doen\u00e7a da ferroportina forma B \u00e9 mais rara e se assemelha \u00e0 hemocromatose tipo 1, mas pode afetar crian\u00e7as."},"en":{"language":"en","value":"Hemochromatosis type 4 (also called ferroportin disease) is a rare form of hereditary hemochromatosis, a group of diseases characterised by excessive tissue iron deposition of genetic origin. It is phenotypically heterogeneous with two sub-types. Ferroportin disease form A is the usual form and is generally asymptomatic with no tissue damage and further complications. Ferroportin disease form B is rarer and resembles hemochromatosis type 1, but can affect children."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"dcad6558d42b616579f6a43219462bd70f6da723","datavalue":{"value":"https://id.who.int/icd/entity/1541297428","type":"string"},"datatype":"url"},"type":"statement","id":"Q97536$C6D2B038-BFCB-40E5-AA11-D42C0C65AD3B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"538cf0d62376f4e7ac6e8432eafb4733ba7ae22d","datavalue":{"value":"CID11:ID_1541297428","type":"string"},"datatype":"string"},"type":"statement","id":"Q97536$98E8992E-5CED-44E1-8A32-C04C95D93FEA","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"9065a438d7c7c128e0f42e247be1552d7db10614","datavalue":{"value":"dki-india-ID_1541297428","type":"string"},"datatype":"string"},"type":"statement","id":"Q97536$28F47D28-BBE9-4787-818A-EF8EAD2C50D2","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q97536$F00B2C31-378C-4A63-BEC9-E263D110FA21","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q97536$59DCCA36-D023-4A58-900B-42E260328C5D","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q97536$2FCACB7A-73CA-420A-9EAB-D8207F48DA63","rank":"normal"}]},"sitelinks":{}}}}