{"entities":{"Q94320":{"pageid":84713,"ns":120,"title":"Item:Q94320","lastrevid":528842,"modified":"2026-08-16T09:27:23Z","type":"item","id":"Q94320","labels":{"mul":{"language":"mul","value":"ID_122234138"},"pt-br":{"language":"pt-br","value":"Disgenesia tubular renal devida \u00e0 transfus\u00e3o entre g\u00eameos"},"en":{"language":"en","value":"Renal tubular dysgenesis due to twin-twin transfusion"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A disgenesia tubular renal devida \u00e0 s\u00edndrome de transfus\u00e3o entre g\u00eameos (s\u00edndrome da transfus\u00e3o feto-fetal [STFF]) \u00e9 uma forma adquirida de disgenesia tubular renal que se desenvolve em fetos de doadores devido ao desvio desigual de fator de crescimento e nutrientes para o rim do receptor e \u00e9 caracterizada por aus\u00eancia ou mal desenvolvimento dos t\u00fabulos proximais, oligoidr\u00e2mnio persistente e consequentemente a sequ\u00eancia de Potter (dismorfismo facial com orelhas grandes e achatadas e com implanta\u00e7\u00e3o baixa, hipoplasia pulmonar, artrogripose e defeitos de posicionamento dos membros)."},"en":{"language":"en","value":"Renal tubular dysgenesis due to twin-twin transfusion syndrome (TTTS) is an acquired form of renal tubular dysgenesis that develops in donor fetuses due to the uneven shunting of growth factor and nutrients to the kidney of the recipient and is characterised by absent or poorly developed proximal tubules, persistent oligohydramnios and consequently the Potter sequence (facial dysmorphism with large and flat low-set ears, lung hypoplasia, arthrogryposis and limb positioning defects)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"9a61afc81b353d46b94ebffed56099962101663d","datavalue":{"value":"https://id.who.int/icd/entity/122234138","type":"string"},"datatype":"url"},"type":"statement","id":"Q94320$FFE60BA6-34E0-48C3-BF29-A088C0F87044","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"e4622d6eb2564406cbfe7fbcd4ba8362fc2af043","datavalue":{"value":"CID11:ID_122234138","type":"string"},"datatype":"string"},"type":"statement","id":"Q94320$C339788D-36A4-4E88-BD54-7D9CF5F77B06","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"7a5409601a3dbdbab2e3236d6cd6905c79220ad3","datavalue":{"value":"dki-india-ID_122234138","type":"string"},"datatype":"string"},"type":"statement","id":"Q94320$26A73E3B-1486-48BD-9323-39F529A6A3A7","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q94320$0A645EC0-0AE6-43CB-9D14-186992B4EE1B","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q94320$BB3B1593-9C39-473B-A3C1-9D5844E61C3C","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q94320$2AF7EB3A-A280-4D94-8CF8-15B33D3E857F","rank":"normal"}]},"sitelinks":{}}}}