{"entities":{"Q94226":{"pageid":84619,"ns":120,"title":"Item:Q94226","lastrevid":528160,"modified":"2026-08-16T09:21:31Z","type":"item","id":"Q94226","labels":{"mul":{"language":"mul","value":"ID_1318015458"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a de Gorham-Stout"},"en":{"language":"en","value":"Gorham-Stout disease"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A doen\u00e7a de Gorham-Stout \u00e9 definida como uma oste\u00f3lise maci\u00e7a, espont\u00e2nea, caracterizada pela prolifera\u00e7\u00e3o local de pequenos vasos sangu\u00edneos ou linf\u00e1ticos, resultando em destrui\u00e7\u00e3o progressiva e reabsor\u00e7\u00e3o \u00f3ssea. Os sinais cl\u00ednicos iniciais incluem dor, edema e fraturas espont\u00e2neas. A oste\u00f3lise pode parar de progredir a qualquer momento, mas muitas vezes o tecido \u00f3sseo desaparece completamente, deixando apenas uma faixa fibrosa residual, um desenvolvimento dram\u00e1tico que inspirou o termo \u201cdoen\u00e7a do osso desaparecido\u201d."},"en":{"language":"en","value":"Gorham-Stout disease is defined as a spontaneous, massive osteolysis characterised by local proliferation of small vascular or lymphatic vessels resulting in progressive destruction and resorption of bone. Clinical signs at presentation include pain, swelling and spontaneous fractures. Osteolysis may stop progressing at any time, but often osseous tissue completely disappears, leaving only a residual fibrous band, a dramatic development inspiring the term 'vanishing bone disease.'"}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"4937f249e8b5cd8af01d2bdbf4e0a85efe7549bf","datavalue":{"value":"https://id.who.int/icd/entity/1318015458","type":"string"},"datatype":"url"},"type":"statement","id":"Q94226$F405DB5E-E457-4A18-B73C-2654D5FF0251","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"3dbe259748ce3098b99d93fe80eeca2be009ca45","datavalue":{"value":"CID11:ID_1318015458","type":"string"},"datatype":"string"},"type":"statement","id":"Q94226$BA9C0498-9305-4794-9EC5-3E260326B37E","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"9a8b8cc4a424d3421ba9fd0762fee626b21139c3","datavalue":{"value":"dki-india-ID_1318015458","type":"string"},"datatype":"string"},"type":"statement","id":"Q94226$60F7F198-C7C3-470A-8758-514E75747DAE","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q94226$C51D09D4-3AAA-4AEB-8C4A-7AF491D43E39","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q94226$45C8EC63-C856-423D-AA04-01EA517A8087","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q94226$FCA8E785-A739-4958-A608-0105166F0976","rank":"normal"}]},"sitelinks":{}}}}