{"entities":{"Q92774":{"pageid":83167,"ns":120,"title":"Item:Q92774","lastrevid":517595,"modified":"2026-08-16T07:54:07Z","type":"item","id":"Q92774","labels":{"mul":{"language":"mul","value":"ID_697826513"},"pt-br":{"language":"pt-br","value":"Miastenia de cinturas n\u00e3o familiar"},"en":{"language":"en","value":"Limb-girdle myasthenia, nonfamilial"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Miastenias de cinturas s\u00e3o condi\u00e7\u00f5es raras nas quais a transmiss\u00e3o neuromuscular prejudicada leva \u00e0 fraqueza dos m\u00fasculos proximais dos membros com pouco ou nenhum envolvimento dos m\u00fasculos oculares, bulbar ou faciais, dando origem a uma marcha caracter\u00edstica de \u201cTrendelenburg\u201d. Na maioria desses pacientes, o in\u00edcio da fraqueza muscular \u00e9 notado pela primeira vez na primeira ou na segunda inf\u00e2ncia, mas um in\u00edcio posterior \u00e9 descrito. A miastenia de cinturas n\u00e3o familial inclui as formas autoimunes."},"en":{"language":"en","value":"Limb-girdle myasthenias are rare conditions in which impaired neuromuscular transmission leads to weakness of proximal limb muscles with little or no involvement of the ocular, bulbar or facial muscles, giving rise to a characteristic \u201cwaddling\u201d gait. In most of these patients the onset of muscle weakness is first noticed in infancy or childhood, but a later onset is described. Nonfamilial limb-girdle myasthenia include autoimmune forms."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"9161f750494678a0fc17ef3cf3426f69e870e0ee","datavalue":{"value":"https://id.who.int/icd/entity/697826513","type":"string"},"datatype":"url"},"type":"statement","id":"Q92774$D67EE832-3BD4-40B8-9D90-042A69BD29D3","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"8a9b2cd05c62522cd91e31d685450aa53dc44368","datavalue":{"value":"CID11:ID_697826513","type":"string"},"datatype":"string"},"type":"statement","id":"Q92774$8C999D64-331E-42C3-AEA5-D02ADD3AE39C","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"9e1721a8c02b980cde2d8293e1e0a7920265738c","datavalue":{"value":"dki-india-ID_697826513","type":"string"},"datatype":"string"},"type":"statement","id":"Q92774$2AB7AD88-F766-49E7-959B-3B21F4E48BFB","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q92774$20EF640E-5E99-41DB-A18C-6336F0E03CB3","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q92774$8BF89BD5-CA30-4CFB-9A14-89D2794EECA8","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q92774$F3AE1020-50C6-44BF-9110-8A526A65B674","rank":"normal"}]},"sitelinks":{}}}}