{"entities":{"Q92409":{"pageid":82802,"ns":120,"title":"Item:Q92409","lastrevid":514941,"modified":"2026-08-16T07:33:07Z","type":"item","id":"Q92409","labels":{"mul":{"language":"mul","value":"ID_2138563851"},"pt-br":{"language":"pt-br","value":"Xantogranuloma necrobi\u00f3tico"},"en":{"language":"en","value":"Necrobiotic xanthogranuloma"}},"descriptions":{"pt-br":{"language":"pt-br","value":"O xantogranuloma necrobi\u00f3tico (XGN) \u00e9 uma doen\u00e7a histioc\u00edtica multissist\u00eamica rara envolvendo a pele na qual n\u00f3dulos e placas xantomatosos infiltrados disseminados est\u00e3o associados na maioria dos casos com paraproteinemia e uma variedade de dist\u00farbios linfoproliferativos subjacentes, incluindo mieloma. O XGN difere da xantomatose difusa plana normolipid\u00eamica, na qual as les\u00f5es cut\u00e2neas s\u00e3o palpavelmente infiltradas e elevadas, em vez de planas e difusas naquela necrobiose, e c\u00e9lulas gigantes de Touton est\u00e3o presentes histologicamente."},"en":{"language":"en","value":"Necrobiotic xanthogranuloma (NXG) is a rare multisystem histiocytic disease involving the skin in which widespread infiltrated xanthomatous nodules and plaques are associated in the majority of cases with paraproteinaemia and a variety of underlying lymphoproliferative disorders including myeloma. NXG differs from diffuse normolipidaemic plane xanthomatosis in that the skin lesions are palpably infiltrated and elevated rather than flat and diffuse and in that necrobiosis and Touton giant cells are present histologically."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"68875dbc6396645aa019b8d7c81663351dd17b03","datavalue":{"value":"https://id.who.int/icd/entity/2138563851","type":"string"},"datatype":"url"},"type":"statement","id":"Q92409$9E021596-D89F-46F0-97BD-C2F28E709012","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"3c6bc355999e1be25ec76bd1f72702246af1c923","datavalue":{"value":"CID11:ID_2138563851","type":"string"},"datatype":"string"},"type":"statement","id":"Q92409$7BE27033-3343-4D0A-8ED3-578A56CA09C6","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"b0a74cbcb262e53029c523cdd57645eaaa4a8457","datavalue":{"value":"dki-india-ID_2138563851","type":"string"},"datatype":"string"},"type":"statement","id":"Q92409$88C51726-DB6B-4170-BADC-19CC1E4B739C","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q92409$BDCDCF9D-4BF9-476E-A070-FC0A35E8CD5F","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q92409$245A6C76-2107-4027-A9CF-91B8A93297CB","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q92409$3747115C-379C-4171-BB74-3318A729416A","rank":"normal"}]},"sitelinks":{}}}}