{"entities":{"Q91643":{"pageid":82036,"ns":120,"title":"Item:Q91643","lastrevid":509879,"modified":"2026-08-15T18:40:34Z","type":"item","id":"Q91643","labels":{"mul":{"language":"mul","value":"ID_1319771917"},"pt-br":{"language":"pt-br","value":"Pneumonia intersticial n\u00e3o espec\u00edfica idiop\u00e1tica"},"en":{"language":"en","value":"Idiopathic non-specific interstitial pneumonia"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Pneumonia intersticial n\u00e3o espec\u00edfica idiop\u00e1tica \u00e9 um tipo de pneumonia intersticial idiop\u00e1tica (PII). A pneumonia intersticial n\u00e3o espec\u00edfica idiop\u00e1tica tem sido associada a v\u00e1rias condi\u00e7\u00f5es m\u00e9dicas, embora um link causal n\u00e3o tenha sido identificado. Al\u00e9m disto, ela pode ser idiop\u00e1tica. O nome pneumonia intersticial n\u00e3o espec\u00edfica (PINE) se originou como uma categoria histopatol\u00f3gica reservada para casos em que a bi\u00f3psia pulmonar cir\u00fargica n\u00e3o demonstrava um padr\u00e3o claramente identific\u00e1vel. O padr\u00e3o histopatol\u00f3gico de PINE \u00e9 encontrado em uma grande variedade de doen\u00e7as de causa conhecida (p.ex., pneumonite de hipersensibilidade, doen\u00e7as relacionadas a drogas, s\u00edndrome da imunodefici\u00eancia adquirida [SIDA] e doen\u00e7as col\u00e1geno-vasculares). Ainda, muitos pacientes diagnosticados com PINE idiop\u00e1tica preenchem crit\u00e9rios para a defini\u00e7\u00e3o de casos de doen\u00e7a indiferenciada do tecido conjuntivo, sugerindo que a PINE idiop\u00e1tica poderia ser, na realidade, uma doen\u00e7a autoimune. Al\u00e9m disto, estima-se que 15 a 20% dos pacientes que se apresentam com DIP (doen\u00e7a pulmonar intersticial) cr\u00f4nica t\u00eam uma doen\u00e7a do tecido conjuntivo oculta ou desenvolvem subsequentemente um quadro claro de doen\u00e7a do tecido conjuntivo. Neste grupo particular de pacientes, a apresenta\u00e7\u00e3o cl\u00ednica inicial pode ser essencialmente indistingu\u00edvel daquela de v\u00e1rias PII (especialmente PINE e PIU)"},"en":{"language":"en","value":"Idiopathic nonspecific interstitial pneumonia is one type of idiopathic interstitial pneumonias (IIPs). Idiopathic nonspecific interstitial pneumonia has been associated with many medical conditions, although a causal link has not been identified. In addition, it may be idiopathic. Nonspecific Interstitial Pneumonia(NSIP) originated as a histopathologic categorization reserved for surgical lung biopsies not demonstrating a clearly identifiable pattern. The histopathologic pattern of NSIP is found in a wide variety of diseases of known cause (e.g., hypersensitivity pneumonitis, drug-related, acquired immunodeficiency syndrome [AIDS]\u2013related, and collagen-vascular diseases). Moreover, many patients diagnosed with idiopathic NSIP meet the case definition of undifferentiated connective tissue disease, suggesting that idiopathic NSIP might actually be an autoimmune disease. In addition, it is estimated that up to 15% to 20% of patients who present with a chronic ILD either have an occult connective tissue disease or subsequently develop a clinically overt connective tissue disease. In this particular group of patients, the initial clinical presentation may be essentially indistinguishable from that of several IIPs (especially NSIP and UIP)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"c83167473502e5bfac8ea3b776fdb43c1881ba5b","datavalue":{"value":"https://id.who.int/icd/entity/1319771917","type":"string"},"datatype":"url"},"type":"statement","id":"Q91643$DE555622-6722-4BBB-B7B0-C42D3FB2FB3B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"243988d1785cd87e2ba4536535f80b3c74b3bcdf","datavalue":{"value":"CID11:ID_1319771917","type":"string"},"datatype":"string"},"type":"statement","id":"Q91643$7A029542-F7EA-439B-8E8A-86235506EDCA","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"d943bd709cc714ab5c6122de5596ddd7c9ec3f17","datavalue":{"value":"dki-india-ID_1319771917","type":"string"},"datatype":"string"},"type":"statement","id":"Q91643$603AB9DD-C646-41E0-A98B-275F3D15CD0E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q91643$3DB616A2-1891-4D9F-8736-5A9A6E9D1696","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q91643$678BABC7-5471-40D5-9516-302BCD92A3A0","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q91643$4BB3A5D7-F237-4BB3-BBA5-78CACD0DCD69","rank":"normal"}]},"sitelinks":{}}}}