{"entities":{"Q90429":{"pageid":80819,"ns":120,"title":"Item:Q90429","lastrevid":501079,"modified":"2026-08-15T17:24:12Z","type":"item","id":"Q90429","labels":{"mul":{"language":"mul","value":"ID_1675893580"},"pt-br":{"language":"pt-br","value":"Xantin\u00faria tipo 2"},"en":{"language":"en","value":"Xanthinuria type 2"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A xantin\u00faria tipo II, um tipo de xantin\u00faria cl\u00e1ssica, \u00e9 um dist\u00farbio autoss\u00f4mico recessivo raro do metabolismo das purinas caracterizado pela defici\u00eancia de xantina desidrogenase e alde\u00eddo oxidase, levando \u00e0 forma\u00e7\u00e3o de urolit\u00edase de xantina urin\u00e1ria e levando, em alguns pacientes, \u00e0 insufici\u00eancia renal. Outras manifesta\u00e7\u00f5es menos comuns incluem artropatia, miopatia e \u00falcera duodenal, enquanto alguns pacientes permanecem assintom\u00e1ticos."},"en":{"language":"en","value":"Type II xanthinuria, a type of classical xanthinuria, is a rare autosomal recessive disorder of purine metabolism characterised by the deficiency of both xanthine dehydrogenase and aldehyde oxidase, leading to the formation of urinary xanthine urolithiasis and leading, in some patients, to kidney failure. Other less common manifestations include arthropathy, myopathy and duodenal ulcer, while some patients remain asymptomatic."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"6183363f2e84ea5d592e65db1f3df2fa7d63eaf4","datavalue":{"value":"https://id.who.int/icd/entity/1675893580","type":"string"},"datatype":"url"},"type":"statement","id":"Q90429$4FA14F9D-765D-4145-B7C1-14F35333550B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"59ee05e1f88413e78d72c52f364e0831d154e4b7","datavalue":{"value":"CID11:ID_1675893580","type":"string"},"datatype":"string"},"type":"statement","id":"Q90429$D304146E-B007-4878-A525-DC0721AD98BE","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"f4afb931963786dbd2fa1c1176271c8719ac2ac9","datavalue":{"value":"dki-india-ID_1675893580","type":"string"},"datatype":"string"},"type":"statement","id":"Q90429$8A146F45-D645-4C54-B34B-1221A49A868E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q90429$F1563F09-45D2-464F-BD0F-39357E34E65F","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q90429$A5145AEB-EEE0-4DAD-9F6F-9AA076B63A72","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q90429$3FE9CC7A-112C-499C-8070-A04EC0295353","rank":"normal"}]},"sitelinks":{}}}}