{"entities":{"Q89199":{"pageid":79584,"ns":120,"title":"Item:Q89199","lastrevid":492137,"modified":"2026-08-15T15:46:17Z","type":"item","id":"Q89199","labels":{"mul":{"language":"mul","value":"ID_1741015882"},"pt-br":{"language":"pt-br","value":"Hemofilia B moderadamente grave"},"en":{"language":"en","value":"Moderately severe haemophilia B"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Hemofilia B moderadamente grave \u00e9 uma forma de hemofilia B (veja este termo), caracterizada pela defici\u00eancia de fator IX, levando a sangramento anormal como resultado de ferimentos menores ou subsequente a cirurgias ou extra\u00e7\u00f5es dent\u00e1rias. Hemofilia B moderadamente grave responde por cerca de 30% de todos os casos de hemofilia B. A atividade biol\u00f3gica do fator IX encontra-se entre 1% e 5%. Hemorragias espont\u00e2neas s\u00e3o raras. A transmiss\u00e3o \u00e9 recessiva ligada ao X, e o transtorno \u00e9 causado por muta\u00e7\u00f5es no gene F9 (Xq28), que codifica o fator IX da coagula\u00e7\u00e3o."},"en":{"language":"en","value":"Moderately severe haemophilia B is a form of haemophilia B (see this term) characterised by factor IX deficiency leading to abnormal bleeding as a result of minor injuries, or following surgery or tooth extraction. Moderately severe haemophilia B accounts for around 30% of all cases of haemophilia B. The biological activity of factor IX is between 1% and 5%. Spontaneous haemorrhages are rare. Transmission is X-linked recessive and the disorder is caused by mutations in the F9 gene (Xq28) encoding coagulation factor IX."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"19ea84d6e1b190d1f684c6ee94cf725e29072e0c","datavalue":{"value":"https://id.who.int/icd/entity/1741015882","type":"string"},"datatype":"url"},"type":"statement","id":"Q89199$3050F8B9-BB71-42A7-9EEC-0506585D5C7B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"da26e3ae38445c464ee83ad155cdc2405d2a23b9","datavalue":{"value":"CID11:ID_1741015882","type":"string"},"datatype":"string"},"type":"statement","id":"Q89199$D40A7CB4-BDCC-4D14-8902-216DB2CB138A","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"6e67e828277a1e010c4b65e6b73fe9599782a044","datavalue":{"value":"dki-india-ID_1741015882","type":"string"},"datatype":"string"},"type":"statement","id":"Q89199$B42EEBDA-B7BA-4155-98BF-8FE13CDC3BBB","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q89199$CDC7FFA4-BD62-4F65-A4D5-776198C8ACE0","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q89199$61FBFE9C-8CC8-449E-BC34-0703C29F5BCE","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q89199$1C6CF64D-A12C-4ED4-8A92-F5FEBD08CA6B","rank":"normal"}]},"sitelinks":{}}}}