{"entities":{"Q89198":{"pageid":79583,"ns":120,"title":"Item:Q89198","lastrevid":492129,"modified":"2026-08-15T15:46:13Z","type":"item","id":"Q89198","labels":{"mul":{"language":"mul","value":"ID_1463993018"},"pt-br":{"language":"pt-br","value":"Forma sintom\u00e1tica de hemofilia B em mulheres portadoras"},"en":{"language":"en","value":"Symptomatic form of haemophilia B in female carriers"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Hemofilia B sintom\u00e1tica em mulheres portadoras \u00e9 um tipo de hemofilia A que se manifesta em algumas mulheres com muta\u00e7\u00f5es no gene F9 (Xq28), que codifica o fator IX da coagula\u00e7\u00e3o. Os sintomas incluem sangramento anormal como resultado de ferimentos leves ou subsequente a cirurgias ou extra\u00e7\u00f5es dent\u00e1rias. Hemorragias espont\u00e2neas podem ocorrer ocasionalmente. A transmiss\u00e3o \u00e9 recessiva ligada ao X."},"en":{"language":"en","value":"Symptomatic haemophilia B in female carriers is a form of haemophilia B that manifests in some women with mutations in the F9 gene (Xq28), encoding coagulation factor IX. Symptoms include abnormal bleeding as a result of minor injuries, or following surgery or tooth extraction. Spontaneous haemorrhages may occur occasionally. Transmission is X-linked recessive."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"877cfe14800ec8dd24debd29b2a1486b4bb95ec2","datavalue":{"value":"https://id.who.int/icd/entity/1463993018","type":"string"},"datatype":"url"},"type":"statement","id":"Q89198$CB908F2C-DFA0-419D-84EC-4C221F5AD603","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"de9b02bdb91175a7ce95f00e2329d0dbb20c0b8c","datavalue":{"value":"CID11:ID_1463993018","type":"string"},"datatype":"string"},"type":"statement","id":"Q89198$50663ABC-E6DC-4A50-8EF3-42755E3EEB13","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"16592b06af890ed3169b3fa3710f0a0a6df111a0","datavalue":{"value":"dki-india-ID_1463993018","type":"string"},"datatype":"string"},"type":"statement","id":"Q89198$F070D14F-A8EA-4587-9BBD-5237197178A2","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q89198$38BC6775-9D46-41E6-95EA-C4B4E3097FCD","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q89198$63C52AC3-FDD8-4833-9FF8-B1699E9BA568","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q89198$2537091E-EA9A-4C15-9983-EDB4FBCB524F","rank":"normal"}]},"sitelinks":{}}}}