{"entities":{"Q88362":{"pageid":78747,"ns":120,"title":"Item:Q88362","lastrevid":486013,"modified":"2026-08-15T14:33:41Z","type":"item","id":"Q88362","labels":{"mul":{"language":"mul","value":"ID_280808713"},"pt-br":{"language":"pt-br","value":"Artropatia progressiva pseudo-reumatoide da inf\u00e2ncia"},"en":{"language":"en","value":"Progressive pseudorheumatoid arthropathy of childhood"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A artropatia (displasia) progressiva pseudo-reumatoide da inf\u00e2ncia (PPD) se apresenta como displasia espondiloepifis\u00e1ria (SED) tardia com artropatia progressiva e \u00e9 descrita como um subtipo autoss\u00f4mico recessivo espec\u00edfico de SED. Tipicamente, n\u00e3o h\u00e1 sintomas no per\u00edodo neonatal. Os sinais mais comuns no momento do diagn\u00f3stico s\u00e3o arqueamento das pernas, fraqueza muscular, edema sim\u00e9trico das articula\u00e7\u00f5es interfalangianas proximais. Limita\u00e7\u00e3o da amplitude de movimento, deformidades e dor se desenvolvem gradualmente e se espalham para outras articula\u00e7\u00f5es. Muitos pacientes t\u00eam envolvimento da coluna vertebral manifestando-se como lordose lombar exagerada, cifose tor\u00e1cica e/ou escoliose."},"en":{"language":"en","value":"Progressive pseudorheumatoid arthropathy (dysplasia) of childhood (PPAC; PPD) presents as spondyloepiphyseal dysplasia (SED) tarda with progressive arthropathy and is described as a specific autosomal recessive subtype of SED. Typically, there are no symptoms in the newborn period. The most common signs at diagnosis are bowing of the legs, muscle weakness, symmetric swelling of the proximal interphalangeal joints. Motion range limitation, deformities and pain develop gradually, and spread to other joints. Many patients have spinal involvement manifesting as exaggerated lumbar lordosis, thoracic kyphosis, and/or scoliosis."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"4046fa93d04053cca7355b06a3f208dbee381b85","datavalue":{"value":"https://id.who.int/icd/entity/280808713","type":"string"},"datatype":"url"},"type":"statement","id":"Q88362$B6333409-DE84-41DF-8506-FCA8FB6FB406","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"d6c195b922739c9f8db004b1151ca3886c6ea38c","datavalue":{"value":"CID11:ID_280808713","type":"string"},"datatype":"string"},"type":"statement","id":"Q88362$5303407D-CA02-4800-8327-66C5C5EE36F3","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"e0c4ccebb72da017e7bbe293103f78e21a04b2fb","datavalue":{"value":"dki-india-ID_280808713","type":"string"},"datatype":"string"},"type":"statement","id":"Q88362$E8FCB288-70E6-4CF2-829C-6D085672A7AA","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q88362$D6BD209F-E6BB-4857-9A32-1FDF7627FD7E","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q88362$549103EA-338B-4B89-8DD6-BE84B137856E","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q88362$925E4B88-B1A6-4B26-A2B5-95D2DFD80AC3","rank":"normal"}]},"sitelinks":{}}}}