{"entities":{"Q87934":{"pageid":78319,"ns":120,"title":"Item:Q87934","lastrevid":482942,"modified":"2026-08-15T13:59:35Z","type":"item","id":"Q87934","labels":{"mul":{"language":"mul","value":"ID_1293848111"},"pt-br":{"language":"pt-br","value":"Purpura fulminans"},"en":{"language":"en","value":"Purpura fulminans"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Purpura fulminans \u00e9 um transtorno tromb\u00f3tico rapidamente progressivo potencialmente fatal afetando principalmente neonatos e crian\u00e7as, caracterizado por les\u00f5es cut\u00e2neas purp\u00faricas e coagula\u00e7\u00e3o intravascular disseminada. As les\u00f5es s\u00e3o inicialmente m\u00e1culas eritematosas bem demarcadas, desenvolvendo rapidamente \u00e1reas centrais irregulares de necrose hemorr\u00e1gica negro-azulada, tornando-se dolorosas, escuras e elevadas, \u00e0s vezes com forma\u00e7\u00e3o de ves\u00edculas ou bolhas. As les\u00f5es posteriormente levam a les\u00e3o isqu\u00eamica endotelial irrevers\u00edvel com necrose gangrenosa. A p\u00farpura fulminante pode progredir rapidamente para fal\u00eancia de m\u00faltiplos \u00f3rg\u00e3os por oclus\u00e3o tromb\u00f3tica de vasos sangu\u00edneos pequenos e m\u00e9dios. Existem tr\u00eas formas classificadas por mecanismo desencadeante: neonatal, infecciosa aguda (a forma mais comum) e idiop\u00e1tica."},"en":{"language":"en","value":"Purpura fulminans is a life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children, characterised by purpuric skin lesions and disseminated intravascular coagulation. The lesions are initially well-demarcated erythematous macules, rapidly developing irregular central areas of blue-black haemorrhagic necrosis, becoming painful, dark and raised, sometimes with vesicle or bulla formation. Lesions later lead to irreversible endothelial ischemic injury with gangrenous necrosis. Purpura fulminans may progress rapidly to multi-organ failure by thrombotic occlusion of small and medium-sized blood vessels. There are three forms classified by triggering mechanism: neonatal, acute infectious (the most common form), and idiopathic."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"1da98463e6bf20d578e5ed6dbb3cf972a8469d11","datavalue":{"value":"https://id.who.int/icd/entity/1293848111","type":"string"},"datatype":"url"},"type":"statement","id":"Q87934$1168BB62-97A0-41F3-887E-37F33C4CEBD3","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"91ec658e6a7539574c4f9677836c35a08a16408b","datavalue":{"value":"CID11:ID_1293848111","type":"string"},"datatype":"string"},"type":"statement","id":"Q87934$D00FC219-591E-4AB7-950A-9011F8BA80E6","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"48b3fbe7e39b10977da870149872d92c9cd216da","datavalue":{"value":"dki-india-ID_1293848111","type":"string"},"datatype":"string"},"type":"statement","id":"Q87934$8FCF6340-1EB1-4018-B9EB-EE7927F32BA4","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q87934$69CD241E-4828-4097-856E-654866945AE1","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q87934$9B6A05DF-4509-4F6D-AA47-E6A0895F8E84","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q87934$3C7D63B7-0FC1-4D90-9940-7BAD8408B3D2","rank":"normal"}]},"sitelinks":{}}}}