{"entities":{"Q86927":{"pageid":77312,"ns":120,"title":"Item:Q86927","lastrevid":475617,"modified":"2026-08-15T12:30:00Z","type":"item","id":"Q86927","labels":{"mul":{"language":"mul","value":"ID_770282867"},"pt-br":{"language":"pt-br","value":"Complexo de esclerose lateral amiotr\u00f3fica-parkinsonismo-dem\u00eancia da Pen\u00ednsula de Kii"},"en":{"language":"en","value":"Amyotrophic lateral sclerosis-parkinsonism-dementia complex of Kii Peninsula"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Um foco de alta preval\u00eancia de ELA e CPD foi identificado na pen\u00ednsula Kii do Jap\u00e3o. As manifesta\u00e7\u00f5es cl\u00ednicas s\u00e3o semelhantes \u00e0s da doen\u00e7a observada em Guam. A expans\u00e3o C9ORF72 foi identificada em 20% dos pacientes com ELA, uma muta\u00e7\u00e3o n\u00e3o detectada nas popula\u00e7\u00f5es de Guam, mas outras causas gen\u00e9ticas n\u00e3o foram identificadas."},"en":{"language":"en","value":"A high-prevalence focus of ALS and PDC has been identified in the Kii peninsula of Japan. Clinical features are similar to the disease noted in Guam. The C9ORF72 expansion was identified in 20% of patients with ALS, a mutation not detected in Guam populations, but other genetic causes have not been identified."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"1b25cb0dd09d1e9a1fb03ce4d5a339c1134a8e01","datavalue":{"value":"https://id.who.int/icd/entity/770282867","type":"string"},"datatype":"url"},"type":"statement","id":"Q86927$B72301EF-A66B-4EE4-AE53-BA16312D81FB","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"fb28ca7c36b005d69d4a484f1138b0b50c48197c","datavalue":{"value":"CID11:ID_770282867","type":"string"},"datatype":"string"},"type":"statement","id":"Q86927$0BF67F27-D4B6-496B-A761-A48D5D436DC0","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"7f71075e27220bd4d0c7a9f01af9a59be66bc0bb","datavalue":{"value":"dki-india-ID_770282867","type":"string"},"datatype":"string"},"type":"statement","id":"Q86927$3C3E02B4-0EF2-4A46-9F6B-5C7456DEA230","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q86927$4062E4D7-0D7D-4D6A-81E3-C09D4CA6D989","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q86927$80B8C2BE-34A0-46AE-9DCB-BA2106AA81A2","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q86927$5385A336-4C39-477A-8B8A-FC24AE525277","rank":"normal"}]},"sitelinks":{}}}}