{"entities":{"Q86679":{"pageid":77064,"ns":120,"title":"Item:Q86679","lastrevid":473798,"modified":"2026-08-15T12:08:00Z","type":"item","id":"Q86679","labels":{"mul":{"language":"mul","value":"ID_470720333"},"pt-br":{"language":"pt-br","value":"Dermatose bolhosa linear por IgA da inf\u00e2ncia"},"en":{"language":"en","value":"Childhood linear IgA bullous dermatosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A dermatose bolhosa linear por IgA infantil \u00e9 uma doen\u00e7a autoimune da pele caracterizada por bolhas na pele e nas mucosas. As causas exatas da doen\u00e7a s\u00e3o desconhecidas, mas a doen\u00e7a \u00e9 mediada por autoanticorpos IgA para hemidesmossomas e componentes da membrana basal BP180 e seu ectodom\u00ednio, BP230 e LAD285. A doen\u00e7a afeta crian\u00e7as, muitas vezes em idade pr\u00e9-escolar. Aqueles raros pacientes com envolvimento de mucosa muito proeminente com cicatrizes s\u00e3o agora classificados como penfigoide de membrana mucosa."},"en":{"language":"en","value":"Childhood linear\u00a0IgA\u00a0bullous\u00a0dermatosis is an autoimmune skin disease characterised by blisters on the skin and mucous membranes. The exact causes of the disease are unknown but the disease is mediated by IgA autoantibodies to hemidesmosome and basement membrane components BP180 and its shed ectodomain, BP230 and LAD285. The disease affects children, often of preschool age. Those rare patients with very prominent mucosal involvement with scarring are now classified as mucous membrane pemphigoid."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"372a7d2cdb138c2824faef57f4e0f970de6e28d7","datavalue":{"value":"https://id.who.int/icd/entity/470720333","type":"string"},"datatype":"url"},"type":"statement","id":"Q86679$721CED1D-52D9-45A2-93E1-658B1966D574","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"064b58e1a3fdd22810865e13e8521d262c013db7","datavalue":{"value":"CID11:ID_470720333","type":"string"},"datatype":"string"},"type":"statement","id":"Q86679$21BB094D-1BDC-432D-A0F1-0A53A2ED0225","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"de9f9418e35978c8ea06a85403cd87ee7354eaaf","datavalue":{"value":"dki-india-ID_470720333","type":"string"},"datatype":"string"},"type":"statement","id":"Q86679$B1E7E0A7-2812-4AB9-8A71-F3EFDC2AE74F","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q86679$4D7FF8C8-02A9-4DDF-92DA-FCDFFC713E60","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q86679$2A65C6AD-841E-4334-A1FE-B402036BB6B1","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q86679$48720BC0-AD05-48F0-A81E-E181F75B3F92","rank":"normal"}]},"sitelinks":{}}}}