{"entities":{"Q86056":{"pageid":76441,"ns":120,"title":"Item:Q86056","lastrevid":469243,"modified":"2026-08-15T11:25:17Z","type":"item","id":"Q86056","labels":{"mul":{"language":"mul","value":"ID_667751114"},"pt-br":{"language":"pt-br","value":"Distrofia muscular de cinturas 2F, defici\u00eancia de delta-sarcoglicano"},"en":{"language":"en","value":"Limb-girdle muscular dystrophy 2F, delta-sarcoglycan deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A distrofia muscular de cinturas autoss\u00f4mica recessiva tipo 2F ou delta-sarcoglicanopatia \u00e9 uma distrofia muscular da cintura escapular (LGMD), que \u00e9 um grupo de dist\u00farbios caracterizados por fraqueza muscular progressiva, em que a musculatura p\u00e9lvica ou da cintura escapular est\u00e1 predominantemente ou principalmente envolvida, e \u00e9 caracterizada por asa escapular e hipertrofia da panturrilha com in\u00edcio entre 2 e 10 anos. O envolvimento card\u00edaco ocorre em cerca de 20% dos casos."},"en":{"language":"en","value":"Autosomal recessive limb-girdle muscular dystrophy type 2F, or delta-sarcoglycanopathy is a limb girdle muscular dystrophy (LGMD), which is a group of disorders characterised by progressive muscle weakness, in which the pelvic or shoulder girdle musculature is predominantly or primarily involved, and is characterised by scapular winging and calf hypertrophy with onset between 2 and 10 years. Cardiac involvement occurs in about 20% of cases."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"cff94217630dd06701a0a2a623cd62e9faa13b62","datavalue":{"value":"https://id.who.int/icd/entity/667751114","type":"string"},"datatype":"url"},"type":"statement","id":"Q86056$BFD2C1F9-4030-4ED0-8AF3-03A711A36519","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"b0b79c952b9e2a5cbde4d972adaf4e4a93b97ca7","datavalue":{"value":"CID11:ID_667751114","type":"string"},"datatype":"string"},"type":"statement","id":"Q86056$66560CC5-68FD-43AC-BCDC-3CAA587D784F","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"c10d9e6b9d57d76cf8eed4551ab25222f718d899","datavalue":{"value":"dki-india-ID_667751114","type":"string"},"datatype":"string"},"type":"statement","id":"Q86056$6CBF1349-6CEE-4845-BC04-FDCFE88E6950","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q86056$DAC09D06-5D01-41DE-9E14-C6B746183046","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q86056$53457E51-B799-4B35-A84F-C1FE3307850D","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q86056$765F8481-B599-4FC9-8BD3-5A3A6CDC17DF","rank":"normal"}]},"sitelinks":{}}}}