{"entities":{"Q85554":{"pageid":75939,"ns":120,"title":"Item:Q85554","lastrevid":465600,"modified":"2026-08-15T10:54:54Z","type":"item","id":"Q85554","labels":{"mul":{"language":"mul","value":"ID_1107278535"},"pt-br":{"language":"pt-br","value":"Miopatia distal de Welander"},"en":{"language":"en","value":"Welander distal myopathy"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A miopatia distal de Welander \u00e9 uma miopatia distal lentamente progressiva com in\u00edcio tardio (ap\u00f3s os 40 anos) herdada como um tra\u00e7o autoss\u00f4mico dominante, apresentando-se com dificuldade em realizar habilidades motoras finas com o dedo indicador e o polegar, seguido por progress\u00e3o para todos os m\u00fasculos extensores do dedo e atrofia dos m\u00fasculos intr\u00ednsecos da m\u00e3o. O envolvimento dos membros inferiores ocorre mais tarde."},"en":{"language":"en","value":"Welander distal myopathy is a distal, slowly progressive myopathy with late onset (after the age of 40) inherited as an autosomal dominant trait, presenting with clumsiness in performing fine motor skills with the index finger and thumb followed by progression to all the finger extensor muscles and atrophy of intrinsic hand muscles. Lower limb involvement occurs later."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"fc34eb4a260cda1828068fb068040ce6d4dcc956","datavalue":{"value":"https://id.who.int/icd/entity/1107278535","type":"string"},"datatype":"url"},"type":"statement","id":"Q85554$6D6315EA-521F-4A00-935C-9C5A2364702B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"02c29010351892c7f319a070ba0d5181c81da637","datavalue":{"value":"CID11:ID_1107278535","type":"string"},"datatype":"string"},"type":"statement","id":"Q85554$C702D5F2-849B-4D7C-8F92-288BE3605129","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"bbf28c78355026c6cd3e3328e3b240c57ab65f7e","datavalue":{"value":"dki-india-ID_1107278535","type":"string"},"datatype":"string"},"type":"statement","id":"Q85554$B17721D9-1757-42D4-A993-C37D7F52758E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q85554$442339B9-FCF6-48D3-BE0B-6C3E7AC205C0","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q85554$B1314893-2D37-4A47-8585-B6C14F556B73","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q85554$71523B70-2CAC-448B-A09C-6F1AD9A8A3E6","rank":"normal"}]},"sitelinks":{}}}}