{"entities":{"Q83528":{"pageid":73913,"ns":120,"title":"Item:Q83528","lastrevid":450912,"modified":"2026-08-15T08:53:33Z","type":"item","id":"Q83528","labels":{"mul":{"language":"mul","value":"ID_1948020523"},"pt-br":{"language":"pt-br","value":"Defici\u00eancia da subunidade E3 do complexo piruvato desidrogenase"},"en":{"language":"en","value":"Pyruvate dehydrogenase complex E3 subunit deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A defici\u00eancia de piruvato desidrogenase E3 \u00e9 um subtipo muito raro de defici\u00eancia de piruvato desidrogenase (PDHD), caracterizada por acidose l\u00e1ctica de in\u00edcio precoce e atraso do desenvolvimento, disfun\u00e7\u00e3o neurol\u00f3gica de in\u00edcio tardio ou doen\u00e7a hep\u00e1tica."},"en":{"language":"en","value":"Pyruvate dehydrogenase E3 deficiency is a very rare subtype of pyruvate dehydrogenase deficiency (PDHD, ) characterised by either early-onset lactic acidosis and delayed development, later-onset neurological dysfunction or liver disease."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"7454046b32a0764f194e1e889b93f953b13a046f","datavalue":{"value":"https://id.who.int/icd/entity/1948020523","type":"string"},"datatype":"url"},"type":"statement","id":"Q83528$38C61B7B-EAB8-4E15-AC76-A04C3E089304","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"c44d4c17c35c9a167fba04294aad60b24dd90e31","datavalue":{"value":"CID11:ID_1948020523","type":"string"},"datatype":"string"},"type":"statement","id":"Q83528$EA9CBA3F-B63A-45C6-A5AC-B6461B383D2C","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"498c4cf7b1cd58efa469fdc6e28af139f342235a","datavalue":{"value":"dki-india-ID_1948020523","type":"string"},"datatype":"string"},"type":"statement","id":"Q83528$9405B1E0-DEF0-4086-B270-5E14F3EAF0B4","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q83528$2B52DABF-95B0-44CF-A1BA-37071C85AB3A","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q83528$35218AFF-B8CA-4746-AD2B-60EE241A10A6","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q83528$66444608-FEB3-4837-AC14-DFD45F32C2BD","rank":"normal"}]},"sitelinks":{}}}}