{"entities":{"Q55346":{"pageid":45719,"ns":120,"title":"Item:Q55346","lastrevid":248807,"modified":"2026-08-14T02:59:31Z","type":"item","id":"Q55346","labels":{"mul":{"language":"mul","value":"ID_43465573"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a falciforme da Hb C com crise"},"en":{"language":"en","value":"Sickle cell Hb-C disease with crisis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a causada pela heran\u00e7a de uma muta\u00e7\u00e3o da HbS de um progenitor e de uma muta\u00e7\u00e3o da HbC do outro progenitor. Esta doen\u00e7a \u00e9 caracterizada por hem\u00e1cias anormais r\u00edgidas em forma de foice, com sintomas dependendo da localiza\u00e7\u00e3o de acometimento. Esta doen\u00e7a pode se manifestar com fadiga, falta de ar, tonturas, dores de cabe\u00e7a, palidez de pele ou mucosas e icter\u00edcia. Esta doen\u00e7a \u00e9 confirmada por identifica\u00e7\u00e3o de muta\u00e7\u00e3o da HbS e da HbC por meio de testes gen\u00e9ticos."},"en":{"language":"en","value":"A disease caused by the inheritance of a HbS mutation from one parent and a HbC mutation from the other parent. This disease is characterised by abnormal rigid sickle-shaped red blood cells and crisis, with symptoms depending on the site of involvement. This disease may present with fatigue, shortness of breath, dizziness, headaches, pallor of skin or mucous membranes, and jaundice. This disease is confirmed by identification of HbS and HbC mutation by genetic testing."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"3f2c3ef516fd1078634b410b199cd641f1d5212b","datavalue":{"value":"https://id.who.int/icd/entity/43465573","type":"string"},"datatype":"url"},"type":"statement","id":"Q55346$6FF7C908-2F3E-4507-B96C-AB13F50871B7","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"3ac0188320b42e8e1f3ee0e8359ec25e9fce4ebb","datavalue":{"value":"CID11:ID_43465573","type":"string"},"datatype":"string"},"type":"statement","id":"Q55346$CDF52F8C-1685-4061-B1F5-8A3D686503FB","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"a94f464d5b6e8a0c0c1fafbc8de0c793a0ede34b","datavalue":{"value":"dki-india-ID_43465573","type":"string"},"datatype":"string"},"type":"statement","id":"Q55346$C6399262-DDB3-459D-BDAE-7FFA85EE0920","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q55346$AD277223-25FE-454E-86DA-C189C0B08C50","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q55346$3E38EB70-32EF-41C1-BCFA-4E5ABE0FD00E","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q55346$A594EFD1-A219-45B1-93A1-9955E4491935","rank":"normal"}]},"sitelinks":{}}}}