{"entities":{"Q54556":{"pageid":44929,"ns":120,"title":"Item:Q54556","lastrevid":243187,"modified":"2026-08-14T02:10:59Z","type":"item","id":"Q54556","labels":{"mul":{"language":"mul","value":"ID_1740585991"},"pt-br":{"language":"pt-br","value":"Acondrogenesia tipo 1B"},"en":{"language":"en","value":"Achondrogenesis type 1B"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Acondrogenesia tipo 1B, uma forma de acondrogenesia, \u00e9 uma displasia esquel\u00e9tica letal rara caracterizada por micromelia grave com dedos das m\u00e3os e dos p\u00e9s muito curtos, uma face plana, um pesco\u00e7o curto, tecido mole espessado ao redor do pesco\u00e7o, hipoplasia do t\u00f3rax, abd\u00f4men protuberante, um apar\u00eancia fetal hidr\u00f3pica e caracter\u00edsticas histol\u00f3gicas distintas da cartilagem."},"en":{"language":"en","value":"Achondrogenesis type 1B, a form of achondrogenesis, is a rare lethal skeletal dysplasia characterised by severe micromelia with very short fingers and toes, a flat face, a short neck, thickened soft tissue around the neck, hypoplasia of the thorax, protuberant abdomen, a hydropic fetal appearance and distinctive histological features of the cartilage."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"959e26f4b8f29c4a2a0dbe9ce3d005512e60bbc2","datavalue":{"value":"https://id.who.int/icd/entity/1740585991","type":"string"},"datatype":"url"},"type":"statement","id":"Q54556$3E78FC15-2A29-42B4-A17A-CE76ECB53D3A","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"d33ba5fb38f300e173e3be22ac8e9bacf82bd591","datavalue":{"value":"CID11:ID_1740585991","type":"string"},"datatype":"string"},"type":"statement","id":"Q54556$D90E8598-FA7D-41F0-983D-92880204058A","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"b0ee119e1c6cb604d02c78c5ae343d03fb12b2ad","datavalue":{"value":"dki-india-ID_1740585991","type":"string"},"datatype":"string"},"type":"statement","id":"Q54556$328DB7C9-437B-4E0D-9A85-D4BB9FF408B7","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q54556$B83D1B1B-58B5-418B-A0DD-C3744B3A73EF","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q54556$130667BA-7A23-46BF-9B97-76D8373DD934","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q54556$3AD8907D-006F-40B1-9B3B-163C0445274B","rank":"normal"}]},"sitelinks":{}}}}