@prefix rdf: <http://www.w3.org/1999/02/22-rdf-syntax-ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .
@prefix rdfs: <http://www.w3.org/2000/01/rdf-schema#> .
@prefix owl: <http://www.w3.org/2002/07/owl#> .
@prefix wikibase: <http://wikiba.se/ontology#> .
@prefix skos: <http://www.w3.org/2004/02/skos/core#> .
@prefix schema: <http://schema.org/> .
@prefix cc: <http://creativecommons.org/ns#> .
@prefix geo: <http://www.opengis.net/ont/geosparql#> .
@prefix prov: <http://www.w3.org/ns/prov#> .
@prefix wd: <https://determinar.ia.br/entity/> .
@prefix data: <https://determinar.ia.br/wiki/Special:EntityData/> .
@prefix wds: <https://determinar.ia.br/entity/statement/> .
@prefix wdref: <https://determinar.ia.br/reference/> .
@prefix wdv: <https://determinar.ia.br/value/> .
@prefix wdt: <https://determinar.ia.br/prop/direct/> .
@prefix wdtn: <https://determinar.ia.br/prop/direct-normalized/> .
@prefix p: <https://determinar.ia.br/prop/> .
@prefix ps: <https://determinar.ia.br/prop/statement/> .
@prefix psv: <https://determinar.ia.br/prop/statement/value/> .
@prefix psn: <https://determinar.ia.br/prop/statement/value-normalized/> .
@prefix pq: <https://determinar.ia.br/prop/qualifier/> .
@prefix pqv: <https://determinar.ia.br/prop/qualifier/value/> .
@prefix pqn: <https://determinar.ia.br/prop/qualifier/value-normalized/> .
@prefix pr: <https://determinar.ia.br/prop/reference/> .
@prefix prv: <https://determinar.ia.br/prop/reference/value/> .
@prefix prn: <https://determinar.ia.br/prop/reference/value-normalized/> .
@prefix wdno: <https://determinar.ia.br/prop/novalue/> .

data:Q52672 a schema:Dataset ;
	schema:about wd:Q52672 ;
	cc:license <http://creativecommons.org/publicdomain/zero/1.0/> ;
	schema:softwareVersion "1.0.0" ;
	schema:version "229787"^^xsd:integer ;
	schema:dateModified "2026-08-13T23:58:59Z"^^xsd:dateTime ;
	wikibase:statements "6"^^xsd:integer ;
	wikibase:sitelinks "0"^^xsd:integer ;
	wikibase:identifiers "0"^^xsd:integer .

wd:Q52672 a wikibase:Item ;
	wdt:P68 <https://id.who.int/icd/entity/398872780> ;
	wdt:P67 "CID11:ID_398872780" ;
	wdt:P70 "dki-india-ID_398872780" ;
	wdt:P86 "Concluído" ;
	wdt:P78 <https://pauloleads.com.br/cases-publicos/> ;
	wdt:P80 "2026-08-13T00:00:00Z"^^xsd:dateTime ;
	p:P68 wds:Q52672-A0EB5CCC-BC95-4D4A-ACAA-F40307A0EF78 .

wds:Q52672-A0EB5CCC-BC95-4D4A-ACAA-F40307A0EF78 a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P68 <https://id.who.int/icd/entity/398872780> .

wd:Q52672 p:P67 wds:Q52672-3B174AA2-A14A-42E4-BBCE-880D039B3F1A .

wds:Q52672-3B174AA2-A14A-42E4-BBCE-880D039B3F1A a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P67 "CID11:ID_398872780" .

wd:Q52672 p:P70 wds:Q52672-956EB745-16A1-4923-B5F3-1AB9825DF92B .

wds:Q52672-956EB745-16A1-4923-B5F3-1AB9825DF92B a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P70 "dki-india-ID_398872780" .

wd:Q52672 p:P86 wds:Q52672-3F53C352-C219-4B4A-B68B-DEDD6EF2B35C .

wds:Q52672-3F53C352-C219-4B4A-B68B-DEDD6EF2B35C a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P86 "Concluído" .

wd:Q52672 p:P78 wds:Q52672-075462C8-62E7-4145-B82B-F56A52B4404D .

wds:Q52672-075462C8-62E7-4145-B82B-F56A52B4404D a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P78 <https://pauloleads.com.br/cases-publicos/> .

wd:Q52672 p:P80 wds:Q52672-9BBCBF4F-C5E6-41EC-9EF9-C03133E65F86 .

wds:Q52672-9BBCBF4F-C5E6-41EC-9EF9-C03133E65F86 a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P80 "2026-08-13T00:00:00Z"^^xsd:dateTime ;
	psv:P80 wdv:d79e909cd3fb623a2f2f7e2ef8a5c1a5 .

wd:Q52672 rdfs:label "ID_398872780"@mul ;
	skos:prefLabel "ID_398872780"@mul ;
	schema:name "ID_398872780"@mul ;
	rdfs:label "Doença de Niemann-Pick"@pt-br ;
	skos:prefLabel "Doença de Niemann-Pick"@pt-br ;
	schema:name "Doença de Niemann-Pick"@pt-br ;
	rdfs:label "Niemann-Pick disease"@en ;
	skos:prefLabel "Niemann-Pick disease"@en ;
	schema:name "Niemann-Pick disease"@en ;
	schema:description "A doença de Niemann-Pick é um distúrbio de armazenamento lisossomal autossômico recessivo causado pela atividade deficiente da esfingomielinase ácida, abrangendo duas formas clinicamente distintas: tipo A e tipo B. O tipo A é caracterizado por um início precoce, no primeiro ano de vida, distúrbios digestivos, atraso de crescimento, hepatoesplenomegalia grave e sintomas neurológicos graves (retardo psicomotor, hipotonia). Os transtornos neurológicos graves e as infecções pulmonares levam à morte precoce, geralmente por volta dos 4 anos de idade. No tipo B, o início ocorre em qualquer idade (até a idade adulta) e o sinal mais constante é a hepatoesplenomegalia, que pode estar associada a sintomas pulmonares."@pt-br,
		"Niemann-Pick disease is an autosomal recessive lysosomal storage disorder caused by the deficient activity of acid sphingomyelinase, encompassing two clinically distinct forms: type A and type B. Type A is characterised by an early onset, within the first year of life, digestive disorders, failure to thrive, major hepatosplenomegaly, and severe neurologic symptoms (psychomotor retardation, hypotonia). The severe neurological disorders and pulmonary infections lead to an early death, often around the age of 4. In type B ), onset occurs at any age (until adulthood) and the most constant sign is hepatosplenomegaly, which can be associated with pulmonary symptoms."@en .

wd:P68 a wikibase:Property ;
	rdfs:label "Canonical URI"@en ;
	skos:prefLabel "Canonical URI"@en ;
	schema:name "Canonical URI"@en ;
	rdfs:label "URI"@mul ;
	skos:prefLabel "URI"@mul ;
	schema:name "URI"@mul ;
	schema:description "Canonical and absolute URI that resolves the entity in the semantic web."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#Url> ;
	wikibase:directClaim wdt:P68 ;
	wikibase:claim p:P68 ;
	wikibase:statementProperty ps:P68 ;
	wikibase:statementValue psv:P68 ;
	wikibase:qualifier pq:P68 ;
	wikibase:qualifierValue pqv:P68 ;
	wikibase:reference pr:P68 ;
	wikibase:referenceValue prv:P68 ;
	wikibase:novalue wdno:P68 .

p:P68 a owl:ObjectProperty .

psv:P68 a owl:ObjectProperty .

pqv:P68 a owl:ObjectProperty .

prv:P68 a owl:ObjectProperty .

wdt:P68 a owl:ObjectProperty .

ps:P68 a owl:ObjectProperty .

pq:P68 a owl:ObjectProperty .

pr:P68 a owl:ObjectProperty .

wdno:P68 a owl:Class ;
	owl:complementOf _:876f845b5aa9df46c3769410b4980ef2 .

_:876f845b5aa9df46c3769410b4980ef2 a owl:Restriction ;
	owl:onProperty wdt:P68 ;
	owl:someValuesFrom owl:Thing .

wd:P67 a wikibase:Property ;
	rdfs:label "CURIE"@en ;
	skos:prefLabel "CURIE"@en ;
	schema:name "CURIE"@en ;
	rdfs:label "CURIE"@mul ;
	skos:prefLabel "CURIE"@mul ;
	schema:name "CURIE"@mul ;
	schema:description "Compact URI prefix identifier for serialization in ontologies and RDF."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#String> ;
	wikibase:directClaim wdt:P67 ;
	wikibase:claim p:P67 ;
	wikibase:statementProperty ps:P67 ;
	wikibase:statementValue psv:P67 ;
	wikibase:qualifier pq:P67 ;
	wikibase:qualifierValue pqv:P67 ;
	wikibase:reference pr:P67 ;
	wikibase:referenceValue prv:P67 ;
	wikibase:novalue wdno:P67 .

p:P67 a owl:ObjectProperty .

psv:P67 a owl:ObjectProperty .

pqv:P67 a owl:ObjectProperty .

prv:P67 a owl:ObjectProperty .

wdt:P67 a owl:DatatypeProperty .

ps:P67 a owl:DatatypeProperty .

pq:P67 a owl:DatatypeProperty .

pr:P67 a owl:DatatypeProperty .

wdno:P67 a owl:Class ;
	owl:complementOf _:fb4af2e463edc3c5bcfdd04432e3ed85 .

_:fb4af2e463edc3c5bcfdd04432e3ed85 a owl:Restriction ;
	owl:onProperty wdt:P67 ;
	owl:someValuesFrom owl:Thing .

wd:P70 a wikibase:Property ;
	rdfs:label "Canary Token"@en ;
	skos:prefLabel "Canary Token"@en ;
	schema:name "Canary Token"@en ;
	rdfs:label "Canary Token"@mul ;
	skos:prefLabel "Canary Token"@mul ;
	schema:name "Canary Token"@mul ;
	schema:description "Tracking token intentionally inserted to audit data leaks, scraping, or unauthorized AI usage."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#String> ;
	wikibase:directClaim wdt:P70 ;
	wikibase:claim p:P70 ;
	wikibase:statementProperty ps:P70 ;
	wikibase:statementValue psv:P70 ;
	wikibase:qualifier pq:P70 ;
	wikibase:qualifierValue pqv:P70 ;
	wikibase:reference pr:P70 ;
	wikibase:referenceValue prv:P70 ;
	wikibase:novalue wdno:P70 .

p:P70 a owl:ObjectProperty .

psv:P70 a owl:ObjectProperty .

pqv:P70 a owl:ObjectProperty .

prv:P70 a owl:ObjectProperty .

wdt:P70 a owl:DatatypeProperty .

ps:P70 a owl:DatatypeProperty .

pq:P70 a owl:DatatypeProperty .

pr:P70 a owl:DatatypeProperty .

wdno:P70 a owl:Class ;
	owl:complementOf _:311fb3b1dabc1cc8a6bb7feafe7ab91b .

_:311fb3b1dabc1cc8a6bb7feafe7ab91b a owl:Restriction ;
	owl:onProperty wdt:P70 ;
	owl:someValuesFrom owl:Thing .

wd:P86 a wikibase:Property ;
	rdfs:label "Verification Status"@en ;
	skos:prefLabel "Verification Status"@en ;
	schema:name "Verification Status"@en ;
	rdfs:label "Status de Verificação"@mul ;
	skos:prefLabel "Status de Verificação"@mul ;
	schema:name "Status de Verificação"@mul ;
	schema:description "Current data verification status of the entity."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#String> ;
	wikibase:directClaim wdt:P86 ;
	wikibase:claim p:P86 ;
	wikibase:statementProperty ps:P86 ;
	wikibase:statementValue psv:P86 ;
	wikibase:qualifier pq:P86 ;
	wikibase:qualifierValue pqv:P86 ;
	wikibase:reference pr:P86 ;
	wikibase:referenceValue prv:P86 ;
	wikibase:novalue wdno:P86 .

p:P86 a owl:ObjectProperty .

psv:P86 a owl:ObjectProperty .

pqv:P86 a owl:ObjectProperty .

prv:P86 a owl:ObjectProperty .

wdt:P86 a owl:DatatypeProperty .

ps:P86 a owl:DatatypeProperty .

pq:P86 a owl:DatatypeProperty .

pr:P86 a owl:DatatypeProperty .

wdno:P86 a owl:Class ;
	owl:complementOf _:09f280a5f3614935b96ccb8c5d63b022 .

_:09f280a5f3614935b96ccb8c5d63b022 a owl:Restriction ;
	owl:onProperty wdt:P86 ;
	owl:someValuesFrom owl:Thing .

wd:P78 a wikibase:Property ;
	rdfs:label "Knowledge Architect"@en ;
	skos:prefLabel "Knowledge Architect"@en ;
	schema:name "Knowledge Architect"@en ;
	rdfs:label "Engº de dados"@mul ;
	skos:prefLabel "Engº de dados"@mul ;
	schema:name "Engº de dados"@mul ;
	schema:description "Knowledge engineer responsible for the curation, ontological modeling, and DKI structuring of this record."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#Url> ;
	wikibase:directClaim wdt:P78 ;
	wikibase:claim p:P78 ;
	wikibase:statementProperty ps:P78 ;
	wikibase:statementValue psv:P78 ;
	wikibase:qualifier pq:P78 ;
	wikibase:qualifierValue pqv:P78 ;
	wikibase:reference pr:P78 ;
	wikibase:referenceValue prv:P78 ;
	wikibase:novalue wdno:P78 .

p:P78 a owl:ObjectProperty .

psv:P78 a owl:ObjectProperty .

pqv:P78 a owl:ObjectProperty .

prv:P78 a owl:ObjectProperty .

wdt:P78 a owl:ObjectProperty .

ps:P78 a owl:ObjectProperty .

pq:P78 a owl:ObjectProperty .

pr:P78 a owl:ObjectProperty .

wdno:P78 a owl:Class ;
	owl:complementOf _:2710e6edcea8e899ac7ae90ea2f8757a .

_:2710e6edcea8e899ac7ae90ea2f8757a a owl:Restriction ;
	owl:onProperty wdt:P78 ;
	owl:someValuesFrom owl:Thing .

wd:P80 a wikibase:Property ;
	rdfs:label "Collection date"@en ;
	skos:prefLabel "Collection date"@en ;
	schema:name "Collection date"@en ;
	rdfs:label "data da última verificação"@mul ;
	skos:prefLabel "data da última verificação"@mul ;
	schema:name "data da última verificação"@mul ;
	schema:description "Date the data was last collected or verified."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#Time> ;
	wikibase:directClaim wdt:P80 ;
	wikibase:claim p:P80 ;
	wikibase:statementProperty ps:P80 ;
	wikibase:statementValue psv:P80 ;
	wikibase:qualifier pq:P80 ;
	wikibase:qualifierValue pqv:P80 ;
	wikibase:reference pr:P80 ;
	wikibase:referenceValue prv:P80 ;
	wikibase:novalue wdno:P80 .

p:P80 a owl:ObjectProperty .

psv:P80 a owl:ObjectProperty .

pqv:P80 a owl:ObjectProperty .

prv:P80 a owl:ObjectProperty .

wdt:P80 a owl:DatatypeProperty .

ps:P80 a owl:DatatypeProperty .

pq:P80 a owl:DatatypeProperty .

pr:P80 a owl:DatatypeProperty .

wdno:P80 a owl:Class ;
	owl:complementOf _:66cf0dd736f1df9217b0a14beb1128c8 .

_:66cf0dd736f1df9217b0a14beb1128c8 a owl:Restriction ;
	owl:onProperty wdt:P80 ;
	owl:someValuesFrom owl:Thing .

wdv:d79e909cd3fb623a2f2f7e2ef8a5c1a5 a wikibase:TimeValue ;
	wikibase:timeValue "2026-08-13T00:00:00Z"^^xsd:dateTime ;
	wikibase:timePrecision "11"^^xsd:integer ;
	wikibase:timeTimezone "0"^^xsd:integer ;
	wikibase:timeCalendarModel <http://www.wikidata.org/entity/Q1985727> .
