{"entities":{"Q46560":{"pageid":36931,"ns":120,"title":"Item:Q46560","lastrevid":182224,"modified":"2026-08-13T15:13:09Z","type":"item","id":"Q46560","labels":{"mul":{"language":"mul","value":"LD26.41"},"pt-br":{"language":"pt-br","value":"Artrogripose m\u00faltipla cong\u00eanita"},"en":{"language":"en","value":"Arthrogryposis multiplex congenita"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Artrogripose m\u00faltipla cong\u00eanita compreende condi\u00e7\u00f5es cong\u00eanitas n\u00e3o progressivas caracterizadas por m\u00faltiplas contraturas articulares. O termo \u00e9 atualmente usado em conex\u00e3o com um grupo muito heterog\u00eaneo de transtornos que todos incluem m\u00faltiplas contraturas articulares cong\u00eanitas. A principal causa da artrogripose \u00e9 a acinesia fetal devido a anormalidades fetais (p.ex., anormalidades neurog\u00eanicas, musculares ou do tecido conjuntivo; limita\u00e7\u00f5es mec\u00e2nicas ao movimento) ou transtornos maternos (p.ex., infec\u00e7\u00e3o, drogas, traumatismo, outras doen\u00e7as maternas). Acinesia fetal generalizada tamb\u00e9m pode causar polidr\u00e2mnio, hipoplasia pulmonar, micrognatia, hipertelorismo ocular e cord\u00e3o umbilical curto. A falta de movimento fetal faz com que tecido conjuntivo extra se desenvolva ao redor da articula\u00e7\u00e3o, limitando o movimento e agravando ainda mais a contratura articular."},"en":{"language":"en","value":"Arthrogryposis multiplex congenita, comprises nonprogressive congenital conditions characterised by multiple joint contractures. The term is currently used in connection with a very heterogeneous group of disorders that all include multiple congenital joint contractures. The major cause of arthrogryposis is fetal akinesia due to fetal abnormalities (e.g. neurogenic, muscle, or connective tissue abnormalities; mechanical limitations to movement) or maternal disorders (e.g. infection, drugs, trauma, other maternal illnesses). Generalised fetal akinesia can also lead to polyhydramnios, pulmonary hypoplasia, micrognathia, ocular hypertelorism, and short umbilical cord. Lack of fetal movement causes extra connective tissue to develop around the joint, limiting movement and further aggravating the joint contracture."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"6814df7242534eb8bc3ad98a1f15b5eb81ce3bd9","datavalue":{"value":"https://id.who.int/icd/entity/1930990330","type":"string"},"datatype":"url"},"type":"statement","id":"Q46560$359937CC-22D9-4F8D-B53F-5044C8D14A70","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"cddf0f64b2b2b129de40f26a1977b09080f582df","datavalue":{"value":"CID11:LD26.41","type":"string"},"datatype":"string"},"type":"statement","id":"Q46560$1322C550-7382-4FC3-8B5D-8636A3FAB2F1","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"22955c410792a5496573a6a5ae8f942b585afea9","datavalue":{"value":"dki-india-LD26.41","type":"string"},"datatype":"string"},"type":"statement","id":"Q46560$78ED3258-F34E-40C8-B72B-5D447A4AD035","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46560$735EF416-237D-49D8-AAD3-B1FF947027B4","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46560$D2A4F04A-7763-4D8D-8034-B9D424BC6432","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46560$399C2C4C-04A0-4ECE-960B-B63C8C1B7132","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"f41f4f84171a4e0f68562c7b1e41a0afa61b87a0","datavalue":{"value":{"entity-type":"item","numeric-id":743,"id":"Q743"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46560$70C4E513-0026-40BD-970C-6B8AD4E05FCF","rank":"normal"}]},"sitelinks":{}}}}