{"entities":{"Q46226":{"pageid":36597,"ns":120,"title":"Item:Q46226","lastrevid":179227,"modified":"2026-08-13T14:40:33Z","type":"item","id":"Q46226","labels":{"mul":{"language":"mul","value":"LA8A.3"},"pt-br":{"language":"pt-br","value":"Estenose a\u00f3rtica supravalvar cong\u00eanita"},"en":{"language":"en","value":"Congenital supravalvar aortic stenosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Malforma\u00e7\u00e3o cardiovascular cong\u00eanita com estreitamento da aorta ao n\u00edvel da jun\u00e7\u00e3o sinotubular, que pode se estender at\u00e9 a aorta ascendente._x000D_ _x000D_ Informa\u00e7\u00f5es adicionais: 'Estenose a\u00f3rtica supravalvar cong\u00eanita' \u00e9 descrita como tr\u00eas formas: uma deformidade em ampulheta, uma membrana fibrosa e um estreitamento difuso da aorta ascendente. A estenose a\u00f3rtica supravalvar pode envolver os \u00f3stios das art\u00e9rias coron\u00e1rias e os folhetos a\u00f3rticos podem estar fixados. As art\u00e9rias coron\u00e1rias podem se tornar tortuosas e dilatadas devido a press\u00f5es elevadas e pode ocorrer aterosclerose precoce."},"en":{"language":"en","value":"A congenital cardiovascular malformation with narrowing of the aorta at the level of the sinotubular junction which may extend into the ascending aorta. Additional information: 'Congenital supravalvar aortic stenosis' is described as three forms: an hourglass deformity, a fibrous membrane, and a diffuse narrowing of the ascending aorta. Supravalvar aortic stenosis may involve the coronary artery ostia, and the aortic leaflets may be tethered. The coronary arteries can become tortuous and dilated due to elevated pressures and early atherosclerosis may ensue."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"639437c02a43c2c4f2e1eb6a7b313569c66cddd1","datavalue":{"value":"https://id.who.int/icd/entity/1066595728","type":"string"},"datatype":"url"},"type":"statement","id":"Q46226$C0B188E9-B77C-4B2B-8C70-B8289858EAA2","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"de1c6002b018c72459171bb1403a519840ac527e","datavalue":{"value":"CID11:LA8A.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q46226$C7AD145F-BF35-4A71-B3AB-3355491C0F27","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"ba5ad14d00fb0002121a34342a0aed1194805ec7","datavalue":{"value":"dki-india-LA8A.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q46226$6D7313C0-4435-4197-8512-460266541CB5","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46226$95FF36F7-CF57-4C82-843B-CF6D315AAAED","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46226$3931B367-BDAB-409E-AD68-541B50967CE0","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46226$D87DB74B-13B2-494F-BC5F-9C0362EEDB5D","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"958778c9880c51450b4c9e8a5f2f2c76062c5a24","datavalue":{"value":{"entity-type":"item","numeric-id":21925,"id":"Q21925"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46226$BB7A873F-3DB1-43F1-B6AD-9A20FB54A766","rank":"normal"}]},"sitelinks":{}}}}