{"entities":{"Q46225":{"pageid":36596,"ns":120,"title":"Item:Q46225","lastrevid":179217,"modified":"2026-08-13T14:40:24Z","type":"item","id":"Q46225","labels":{"mul":{"language":"mul","value":"LA8B.22"},"pt-br":{"language":"pt-br","value":"Arco a\u00f3rtico interrompido"},"en":{"language":"en","value":"Interrupted aortic arch"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Malforma\u00e7\u00e3o cardiovascular cong\u00eanita em que h\u00e1 aus\u00eancia de continuidade luminal entre a aorta ascendente e descendente._x000D_ _x000D_ Informa\u00e7\u00f5es adicionais: inclui atresia luminal com descontinuidade entre os segmentos a\u00f3rticos e tamb\u00e9m atresia luminal com continuidade fibrosa entre os segmentos a\u00f3rticos. Arco a\u00f3rtico interrompido \u00e9 definido como a perda da continuidade luminal entre aorta ascendente e descendente. Na maioria dos casos, o fluxo sangu\u00edneo para a aorta tor\u00e1cica descendente ocorre atrav\u00e9s de um ducto arterial patente e h\u00e1 um grande defeito do septo ventricular. A interrup\u00e7\u00e3o do arco \u00e9 adicionalmente definida pela localiza\u00e7\u00e3o de interrup\u00e7\u00e3o._x000D_ _x000D_ No tipo A, a interrup\u00e7\u00e3o \u00e9 distal \u00e0 art\u00e9ria subcl\u00e1via esquerda; no tipo B, a interrup\u00e7\u00e3o \u00e9 entre as art\u00e9rias car\u00f3tida esquerda e subcl\u00e1via esquerda; e no tipo C, a interrup\u00e7\u00e3o ocorre entre as art\u00e9rias inominada e car\u00f3tida esquerda."},"en":{"language":"en","value":"A congenital cardiovascular malformation in which there is an absence of luminal continuity between the ascending and descending aorta. Additional information: this includes luminal atresia with discontinuity between the aortic segments and also luminal atresia with fibrous continuity between the aortic segments. Interrupted aortic arch is defined as the loss of luminal continuity between the ascending and descending aorta. In most cases, blood flow to the descending thoracic aorta is through a patent arterial duct, and there is a large ventricular septal defect. Arch interruption is further defined by site of interruption. In type A, interruption is distal to the left subclavian artery; in type B, interruption is between the left carotid and left subclavian arteries; and in type C, interruption occurs between the innominate and left carotid arteries."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"c11e01bea3a237fdcc970c1f9db254d4e00d1bca","datavalue":{"value":"https://id.who.int/icd/entity/1769930414","type":"string"},"datatype":"url"},"type":"statement","id":"Q46225$0C6BD646-59AA-4040-BD3C-7C2FC641FD63","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"938f968f9ffc5cf053675fc328b7664c631fbd84","datavalue":{"value":"CID11:LA8B.22","type":"string"},"datatype":"string"},"type":"statement","id":"Q46225$8B6BFFEF-01A3-499E-B8A8-2DDD0E84C695","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"41de363c2d376c0f344f3a85e6affa8962d81d2d","datavalue":{"value":"dki-india-LA8B.22","type":"string"},"datatype":"string"},"type":"statement","id":"Q46225$6E72E438-6415-4345-ACE6-781E8E2A4A30","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46225$34B8C470-D3A1-4BA3-AFA2-44304EF29D50","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46225$7A680E25-06EF-4AEB-A615-356554DF249E","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46225$628DC9DC-575A-43EB-BF89-0CFE82F7F8DC","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"fbae82b78a5261cea51b73a640063a287ac3175c","datavalue":{"value":{"entity-type":"item","numeric-id":21924,"id":"Q21924"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46225$347AE34F-EF17-4BFB-A853-C3C5A2C684E7","rank":"normal"}]},"sitelinks":{}}}}