{"entities":{"Q46158":{"pageid":36529,"ns":120,"title":"Item:Q46158","lastrevid":178595,"modified":"2026-08-13T14:33:34Z","type":"item","id":"Q46158","labels":{"mul":{"language":"mul","value":"LA89"},"pt-br":{"language":"pt-br","value":"Cora\u00e7\u00e3o univentricular funcional"},"en":{"language":"en","value":"Functionally univentricular heart"}},"descriptions":{"pt-br":{"language":"pt-br","value":"O termo \u201ccora\u00e7\u00e3o funcionalmente univentricular\u201d descreve um espectro de malforma\u00e7\u00f5es cardiovasculares cong\u00eanitas em que a massa ventricular pode n\u00e3o se prestar facilmente \u00e0 parti\u00e7\u00e3o que aloca uma bomba ventricular para a circula\u00e7\u00e3o sist\u00eamica e outra para a circula\u00e7\u00e3o pulmonar._x000D_ _x000D_ Informa\u00e7\u00f5es adicionais: um cora\u00e7\u00e3o pode ser funcionalmente univentricular devido \u00e0 sua anatomia ou devido \u00e0 falta de viabilidade ou n\u00e3o conveni\u00eancia de dividir cirurgicamente a massa ventricular. Les\u00f5es comuns nesta categoria incluem tipicamente dupla via de entrada do ventr\u00edculo direito (DVEVD), dupla via de entrada do ventr\u00edculo esquerdo (DVEVE), atresia tric\u00faspide, atresia mitral e s\u00edndrome do cora\u00e7\u00e3o esquerdo hipopl\u00e1sico. Outras les\u00f5es que \u00e0s vezes podem ser consideradas um cora\u00e7\u00e3o funcionalmente univentricular incluem formas complexas de defeito do septo atrioventricular, dupla via de sa\u00edda do ventr\u00edculo direito, transposi\u00e7\u00e3o de grandes vasos congenitamente corrigida, atresia pulmonar com septo ventricular \u00edntegro e outras malforma\u00e7\u00f5es cardiovasculares. C\u00f3digos de diagn\u00f3stico espec\u00edficos devem ser usados \u200b\u200bsempre que poss\u00edvel, e n\u00e3o o termo \u201ccora\u00e7\u00e3o funcionalmente univentricular\u201d."},"en":{"language":"en","value":"The term \u201cfunctionally univentricular heart\u201d describes a spectrum of congenital cardiovascular malformations in which the ventricular mass may not readily lend itself to partitioning that commits one ventricular pump to the systemic circulation, and another to the pulmonary circulation. Additional information: a heart may be functionally univentricular because of its anatomy or because of the lack of feasibility or lack of advisability of surgically partitioning the ventricular mass. Common lesions in this category typically include double inlet right ventricle (DIRV), double inlet left ventricle (DILV), tricuspid atresia, mitral atresia, and hypoplastic left heart syndrome. Other lesions which sometimes may be considered to be a functionally univentricular heart include complex forms of atrioventricular septal defect, double outlet right ventricle, congenitally corrected transposition, pulmonary atresia with intact ventricular septum, and other cardiovascular malformations. Specific diagnostic codes should be used whenever possible, and not the term \u201cfunctionally univentricular heart\u201d."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"06f69a7c7f0846fd898b6515769ae7e6de079e23","datavalue":{"value":"https://id.who.int/icd/entity/5417233","type":"string"},"datatype":"url"},"type":"statement","id":"Q46158$4B9C51D2-76AD-4052-AA7D-E540949335CA","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"dd457f17e310d7a1e818e5f1c3133f4ee23a5543","datavalue":{"value":"CID11:LA89","type":"string"},"datatype":"string"},"type":"statement","id":"Q46158$137A9BAC-9C87-4D61-8B45-522822862676","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"1db2601c83d89234eb54b6e62cdc89d12ef88404","datavalue":{"value":"dki-india-LA89","type":"string"},"datatype":"string"},"type":"statement","id":"Q46158$ED8FB5EC-3D3F-4DBD-B5E0-1F0E9EA79C7E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46158$99A3297F-D5A0-48F1-9676-2A309655C8A7","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46158$46478190-382A-4950-A270-08EABCE948D2","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46158$4EB266F2-09EF-4D58-9C93-37D22E2866CB","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"629e829e7264e007295a579b88aa9a2e7af2a032","datavalue":{"value":{"entity-type":"item","numeric-id":209,"id":"Q209"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46158$3403AF64-5C97-4203-83FF-F7446A626A10","rank":"normal"}]},"sitelinks":{}}}}