{"entities":{"Q43943":{"pageid":34311,"ns":120,"title":"Item:Q43943","lastrevid":159281,"modified":"2026-08-13T11:10:48Z","type":"item","id":"Q43943","labels":{"mul":{"language":"mul","value":"EB13"},"pt-br":{"language":"pt-br","value":"S\u00edndrome de Stevens-Johnson ou necr\u00f3lise epid\u00e9rmica t\u00f3xica"},"en":{"language":"en","value":"Stevens-Johnson syndrome or toxic epidermal necrolysis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Espectro de transtornos de hipersensibilidade graves e com risco de vida afetando pele e mucosas, mais comumente precipitados por uma rea\u00e7\u00e3o idiossincr\u00e1tica a medica\u00e7\u00e3o. A s\u00edndrome de Stevens-Johnson (SSJ) sempre envolve superf\u00edcies mucosas, mas o envolvimento da pele est\u00e1 limitado por defini\u00e7\u00e3o a <10% da \u00e1rea de superf\u00edcie corporal (ASC). A necr\u00f3lise epid\u00e9rmica t\u00f3xica (NET) pode \u00e0s vezes poupar as mucosas, mas o envolvimento da pele \u00e9 por defini\u00e7\u00e3o >30% ASC. Uma forma intermedi\u00e1ria \u00e9 reconhecida na qual o envolvimento da mucosa \u00e9 acompanhado pelo envolvimento de 10-30% ASC da pele (s\u00edndrome de sobreposi\u00e7\u00e3o SSJ_NET). Todas as formas resultam em extensa descama\u00e7\u00e3o e ulcera\u00e7\u00e3o e carregam um risco significativo de desfecho fatal."},"en":{"language":"en","value":"A spectrum of severe and life-threatening hypersensitivity disorders affecting skin and mucous membranes, most commonly precipitated by an idiosyncratic reaction to medication. Stevens-Johnson syndrome (SJS) always involves mucosal surfaces but the skin involvement is limited by definition to <10% body surface area (BSA). Toxic epidermal necrolysis (TEN) may sometimes spare mucous membranes but skin involvement is by definition >30% BSA. An intermediate form is recognised in which mucosal involvement is accompanied by skin involvement of 10-30% BSA (SJS-TEN overlap syndrome). All forms result in extensive sloughing and ulceration and carry a significant risk of fatal outcome."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"e50eef767c25b6ec3866eea6d51741cea737f7a1","datavalue":{"value":"https://id.who.int/icd/entity/195467267","type":"string"},"datatype":"url"},"type":"statement","id":"Q43943$40BAD958-2CFA-403D-B827-52C6D192B7A4","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"71098afff23fd1a05d19a05d362c6a8c0a94072e","datavalue":{"value":"CID11:EB13","type":"string"},"datatype":"string"},"type":"statement","id":"Q43943$756034BE-D0FE-4483-931F-FC90EDF0A4B4","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"dc3fb15fc7ba4e2ae8f3e05e37d96efc2a060d4a","datavalue":{"value":"dki-india-EB13","type":"string"},"datatype":"string"},"type":"statement","id":"Q43943$DBC528BD-3CED-4DC0-90D2-32BCD3F1F4D6","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q43943$650A0C2F-1467-49F7-9236-34BD92B5092D","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q43943$E45DA25D-7E85-40E9-B3A9-5CFDD10C5240","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q43943$6FD7F85C-C06A-42D3-AFB0-11CFDCE339A6","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"c668aa4846bd31c8e6d2dc3530f45af5ee3ab8b6","datavalue":{"value":{"entity-type":"item","numeric-id":43939,"id":"Q43939"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q43943$F4965A7D-9B47-46B5-AE51-1679ABD0B7C3","rank":"normal"}]},"sitelinks":{}}}}